Lung transplantation for interstitial lung disease.


Journal

European respiratory review : an official journal of the European Respiratory Society
ISSN: 1600-0617
Titre abrégé: Eur Respir Rev
Pays: England
ID NLM: 9111391

Informations de publication

Date de publication:
30 Sep 2021
Historique:
received: 18 01 2021
accepted: 02 04 2021
entrez: 5 8 2021
pubmed: 6 8 2021
medline: 25 11 2021
Statut: epublish

Résumé

Lung transplantation (LTx) can be a life-extending treatment option for patients with advanced and/or progressive fibrotic interstitial lung disease (ILD), especially idiopathic pulmonary fibrosis (IPF), fibrotic hypersensitivity pneumonitis, sarcoidosis and connective tissue disease-associated ILD. IPF is now the most common indication for LTx worldwide. Several unique features in patients with ILD can impact optimal timing of referral or listing for LTx, pre- or post-transplant risks, candidacy and post-transplant management. As the epidemiology of LTx and community practices have evolved, recent literature describes outcomes and approaches in higher-risk candidates. In this review, we discuss the unique and important clinical findings, course, monitoring and management of patients with IPF and other progressive fibrotic ILDs during pre-LTx evaluation and up to the day of transplantation; the need for co-management with clinical experts in ILD and LTx is emphasised. Some post-LTx complications are unique in these patient cohorts, which require prompt detection and appropriate management by experts in multiple disciplines familiar with telomere biology disorders and infectious, haematological, oncological and cardiac complications to enhance the likelihood of improved outcomes and survival of LTx recipients with IPF and other ILDs.

Identifiants

pubmed: 34348979
pii: 30/161/210017
doi: 10.1183/16000617.0017-2021
pmc: PMC9488499
pii:
doi:

Types de publication

Journal Article Review

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

Copyright ©The authors 2021.

Déclaration de conflit d'intérêts

Conflict of interest: S.G. Kapnadak has nothing to disclose. Conflict of interest: G. Raghu reports personal fees and other funding from Boehringer Ingelheim, and other funding from Roche-Genentech, outside the submitted work.

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Auteurs

Siddhartha G Kapnadak (SG)

Division of Pulmonary, Critical Care and Sleep Medicine, Dept of Medicine, University of Washington, Seattle, WA, USA.

Ganesh Raghu (G)

Division of Pulmonary, Critical Care and Sleep Medicine, Dept of Medicine, University of Washington, Seattle, WA, USA graghu@uw.edu.
Dept of Laboratory Medicine and Pathology, University of Washington, Seattle, WA, USA.

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