Histological activity despite normal ALT and IgG serum levels in patients with autoimmune hepatitis and cirrhosis.

AIH, autoimmune hepatitis ALD, alcoholic liver disease ALP, alkaline phosphatase ALT, alanine aminotransferase AST, aspartate aminotransferase Autoimmune hepatitis Biochemical remission Cirrhosis EASL, European Association for the Study of the Liver Histological activity ICC, intraclass correlation coefficient INR, international normalised ratio LLN, lower limit of normal Liver biopsy MELD, model for end-stage liver disease NAFLD, non-alcoholic fatty liver disease TE, transient elastography TIPS, transjugular intrahepatic portosystemic shunt ULN, upper limit of normal gamma-GT, gamma glutamyl transferase mHAI mHAI, modified Hepatitis Activity Index

Journal

JHEP reports : innovation in hepatology
ISSN: 2589-5559
Titre abrégé: JHEP Rep
Pays: Netherlands
ID NLM: 101761237

Informations de publication

Date de publication:
Aug 2021
Historique:
received: 27 10 2020
revised: 14 05 2021
accepted: 31 05 2021
entrez: 12 8 2021
pubmed: 13 8 2021
medline: 13 8 2021
Statut: epublish

Résumé

In autoimmune hepatitis (AIH), normal levels of transaminases and IgG define biochemical remission and are considered the best surrogate markers for histological remission. This study assessed whether this also applies to patients with AIH cirrhosis. In this European multicentric study, we included 125 biopsies from 113 patients with AIH and histologically proven cirrhosis; 105 biopsies from 104 patients with AIH without cirrhosis served as controls. Biochemical parameters were available within 4 weeks of biopsy. AIH activity was graded according to the modified Hepatitis Activity Index (mHAI), with mHAI ≥4/18 considered to indicate risk of disease progression. In total, 47 out of 125 liver biopsies were obtained from patients with AIH cirrhosis and normal ALT levels at time of biopsy. Only 26% (12/47) of those livers showed histological remission (mHAI <4/18), whereas 36% (17/47) showed moderate to high histological activity (mHAI ≥6/18). In patients with noncirrhotic AIH, 88% (46/52 biopsies) of cases with normal ALT levels had histological remission and only 4% (2/52) had an mHAI ≥6/18 ( In contrast to patients with noncirrhotic AIH, in patients with AIH cirrhosis, who are at risk of disease progression, normal ALT levels and potentially also complete biochemical remission are poor surrogate markers of histological remission. Thus, new biomarkers are needed to monitor disease activity and progression in patients with AIH cirrhosis. Autoimmune hepatitis (AIH) is an inflammatory disease of the liver that usually responds to immunosuppressive therapy. Serum transaminases and IgG levels within the normal ranges define complete biochemical remission and are considered as surrogate markers for histological disease activity. Here, we show that those biochemical markers are not sufficient to indicate low disease activity in patients with AIH and already established cirrhosis. Consequently, until better biomarkers for disease activity are found, only liver biopsy can reliably indicate disease activity in the presence of cirrhosis. Additional investigations, such as measurements of liver stiffness, should be undertaken to monitor non-invasively for disease progression in patients with AIH and established cirrhosis.

Sections du résumé

BACKGROUND & AIMS OBJECTIVE
In autoimmune hepatitis (AIH), normal levels of transaminases and IgG define biochemical remission and are considered the best surrogate markers for histological remission. This study assessed whether this also applies to patients with AIH cirrhosis.
METHODS METHODS
In this European multicentric study, we included 125 biopsies from 113 patients with AIH and histologically proven cirrhosis; 105 biopsies from 104 patients with AIH without cirrhosis served as controls. Biochemical parameters were available within 4 weeks of biopsy. AIH activity was graded according to the modified Hepatitis Activity Index (mHAI), with mHAI ≥4/18 considered to indicate risk of disease progression.
RESULTS RESULTS
In total, 47 out of 125 liver biopsies were obtained from patients with AIH cirrhosis and normal ALT levels at time of biopsy. Only 26% (12/47) of those livers showed histological remission (mHAI <4/18), whereas 36% (17/47) showed moderate to high histological activity (mHAI ≥6/18). In patients with noncirrhotic AIH, 88% (46/52 biopsies) of cases with normal ALT levels had histological remission and only 4% (2/52) had an mHAI ≥6/18 (
CONCLUSIONS CONCLUSIONS
In contrast to patients with noncirrhotic AIH, in patients with AIH cirrhosis, who are at risk of disease progression, normal ALT levels and potentially also complete biochemical remission are poor surrogate markers of histological remission. Thus, new biomarkers are needed to monitor disease activity and progression in patients with AIH cirrhosis.
LAY SUMMARY BACKGROUND
Autoimmune hepatitis (AIH) is an inflammatory disease of the liver that usually responds to immunosuppressive therapy. Serum transaminases and IgG levels within the normal ranges define complete biochemical remission and are considered as surrogate markers for histological disease activity. Here, we show that those biochemical markers are not sufficient to indicate low disease activity in patients with AIH and already established cirrhosis. Consequently, until better biomarkers for disease activity are found, only liver biopsy can reliably indicate disease activity in the presence of cirrhosis. Additional investigations, such as measurements of liver stiffness, should be undertaken to monitor non-invasively for disease progression in patients with AIH and established cirrhosis.

Identifiants

pubmed: 34381983
doi: 10.1016/j.jhepr.2021.100321
pii: S2589-5559(21)00097-5
pmc: PMC8333110
doi:

Types de publication

Journal Article

Langues

eng

Pagination

100321

Informations de copyright

© 2021 The Authors.

Déclaration de conflit d'intérêts

The authors have declared no conflicts of interest.

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Auteurs

Alena Laschtowitz (A)

Department of Medicine, University Medical Centre Hamburg-Eppendorf, Hamburg, Germany.
European Reference Network for Hepatological Diseases (ERN-RARE LIVER).

Kalliopi Zachou (K)

Department of Medicine and Research Laboratory of Internal Medicine, National Expertise Centre of Greece in Autoimmune Liver Diseases, General University Hospital of Larissa, Larissa, Greece.

Vasiliki Lygoura (V)

Department of Medicine and Research Laboratory of Internal Medicine, National Expertise Centre of Greece in Autoimmune Liver Diseases, General University Hospital of Larissa, Larissa, Greece.

Simon Pape (S)

European Reference Network for Hepatological Diseases (ERN-RARE LIVER).
Department of Gastroenterology and Hepatology, Radboud University Medical Centre, Nijmegen, The Netherlands.

Finn Derben (F)

European Reference Network for Hepatological Diseases (ERN-RARE LIVER).
Department of Gastroenterology, Hepatology and Endocrinology, Hannover Medical School, Hannover, Germany.

Elmar Jaeckel (E)

European Reference Network for Hepatological Diseases (ERN-RARE LIVER).
Department of Gastroenterology, Hepatology and Endocrinology, Hannover Medical School, Hannover, Germany.

Sergio Oller-Moreno (S)

Institute of Medical Systems Biology, Centre for Molecular Neurobiology, University Medical Centre Hamburg-Eppendorf, Hamburg, Germany.

Sören Weidemann (S)

European Reference Network for Hepatological Diseases (ERN-RARE LIVER).
Department of Pathology, University Medical Centre Hamburg-Eppendorf, Hamburg, Germany.

Till Krech (T)

Department of Pathology, University Medical Centre Hamburg-Eppendorf, Hamburg, Germany.

Felix Piecha (F)

Department of Medicine, University Medical Centre Hamburg-Eppendorf, Hamburg, Germany.
German Centre for Infection Research (DZIF), Partner Site Hamburg-Lübeck-Borstel-Riems, Hamburg, Germany.

Gerhard Schön (G)

Institute of Medical Biometry and Epidemiology, University Medical Centre Hamburg-Eppendorf, Hamburg, Germany.

Anna-Maria Liebhoff (AM)

Institute of Medical Systems Biology, Centre for Molecular Neurobiology, University Medical Centre Hamburg-Eppendorf, Hamburg, Germany.

Munira Al Tarrah (M)

Institute of Liver Studies and Transplantation, King´s College Hospital, London, UK.

Michael Heneghan (M)

Institute of Liver Studies and Transplantation, King´s College Hospital, London, UK.

Joost P H Drenth (JPH)

European Reference Network for Hepatological Diseases (ERN-RARE LIVER).
Department of Gastroenterology and Hepatology, Radboud University Medical Centre, Nijmegen, The Netherlands.

George Dalekos (G)

Department of Medicine and Research Laboratory of Internal Medicine, National Expertise Centre of Greece in Autoimmune Liver Diseases, General University Hospital of Larissa, Larissa, Greece.

Richard Taubert (R)

European Reference Network for Hepatological Diseases (ERN-RARE LIVER).
Department of Gastroenterology, Hepatology and Endocrinology, Hannover Medical School, Hannover, Germany.

Ansgar Wilhelm Lohse (AW)

Department of Medicine, University Medical Centre Hamburg-Eppendorf, Hamburg, Germany.
European Reference Network for Hepatological Diseases (ERN-RARE LIVER).
German Centre for Infection Research (DZIF), Partner Site Hamburg-Lübeck-Borstel-Riems, Hamburg, Germany.
Hamburg Centre for Translational Immunology (HCTI), University Medical Centre Hamburg-Eppendorf, Hamburg, Germany.

Christoph Schramm (C)

Department of Medicine, University Medical Centre Hamburg-Eppendorf, Hamburg, Germany.
European Reference Network for Hepatological Diseases (ERN-RARE LIVER).
Hamburg Centre for Translational Immunology (HCTI), University Medical Centre Hamburg-Eppendorf, Hamburg, Germany.
Martin Zeitz Centre for Rare Diseases, University Medical Centre Hamburg-Eppendorf, Hamburg, Germany.

Classifications MeSH