Leadless intracardiac transcatheter pacing system: 20 months follow up in adult Duchenne muscular dystrophy.


Journal

Neuromuscular disorders : NMD
ISSN: 1873-2364
Titre abrégé: Neuromuscul Disord
Pays: England
ID NLM: 9111470

Informations de publication

Date de publication:
09 2021
Historique:
received: 14 04 2021
revised: 10 06 2021
accepted: 14 06 2021
pubmed: 16 8 2021
medline: 27 1 2022
entrez: 15 8 2021
Statut: ppublish

Résumé

Duchenne muscular dystrophy (DMD) is an X-linked muscular dystrophy in relation with dystrophin deficient. Heart and respiratory function are classically involved and affect long-term prognosis. Significant atrio-ventricular block may occur in some patients. Implantation of traditional pacemaker may be challenging in patients with tracheotomy and on permanent home mechanical ventilation. We report the first case of a successful leadless intra-cardiac trans-catheter pacing system implantation in an adult DMD on wheelchair and on permanent home mechanical ventilation.

Identifiants

pubmed: 34391632
pii: S0960-8966(21)00162-0
doi: 10.1016/j.nmd.2021.06.008
pii:
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

896-898

Informations de copyright

Copyright © 2021 Elsevier B.V. All rights reserved.

Déclaration de conflit d'intérêts

Declaration of Competing Interest None.

Auteurs

Abdallah Fayssoil (A)

Unité de Cardiologie, Hôpital Raymond Poincaré, APHP, Garches, France; Université de Paris-Saclay, UVSQ, INSERM U1179, END-ICAP, Montigny-le-Bretonneux, France; Service de Cardiologie, Centre de référence des Cardiomyopathies, Hôpital Ambroise Paré, APHP, Boulogne-Billancourt, France. Electronic address: abdallah.fayssoil@aphp.fr.

Arnaud Lazarus (A)

Unité de Rythmologie, Clinique Ambroise Paré, Neuilly sur Seine, France.

Karim Wahbi (K)

Service de Cardiologie, Hôpital Cochin, APHP, Paris, France.

Bernard Clair (B)

Médecine intensive et réanimation, CIC 1429, FHU Phenix, Centre de référence des maladies neuromusculaires, France.

Nicolas Mansencal (N)

Service de Cardiologie, Centre de référence des Cardiomyopathies, Hôpital Ambroise Paré, APHP, Boulogne-Billancourt, France.

David Orlikowski (D)

Médecine intensive et réanimation, CIC 1429, FHU Phenix, Centre de référence des maladies neuromusculaires, France.

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Classifications MeSH