[Rare pancreatic tumors].
Seltene Pankreastumoren.
Acinar cell carcinoma
Differential diagnosis
Molecular pathology
Pancreatoblastoma
Solid pseudopapillary neoplasm
Journal
Der Pathologe
ISSN: 1432-1963
Titre abrégé: Pathologe
Pays: Germany
ID NLM: 8006541
Informations de publication
Date de publication:
Sep 2021
Sep 2021
Historique:
accepted:
06
07
2021
pubmed:
18
8
2021
medline:
1
9
2021
entrez:
17
8
2021
Statut:
ppublish
Résumé
Beyond pancreatic ductal adenocarcinoma, which is by far the most frequent pancreatic neoplasm, a great variety of tumors occur in the pancreas. They include solid and cystic masses and epithelial and nonepithelial neoplasms, and they show a great diversity in their biological behavior, ranging from benign tumors to highly aggressive neoplasms. As examples of rare pancreatic tumors, clinical, morphological, and molecular aspects of acinar cell carcinoma, pancreatoblastoma, solid pseudopapillary neoplasm, and serous cystic neoplasms are presented and discussed. Neben dem weitaus häufigsten Pankreastumor, dem duktalen Adenokarzinom des Pankreas, existieren zahlreiche solide und zystische, epitheliale und nichtepitheliale Tumoren im Pankreas, die für sich genommen jeweils selten sind und klinisch ein breites Spektrum von benignen Tumoren bis zu hochaggressiven, metastasierungs- und rezidivfreudigen Neoplasien abdecken. Exemplarisch werden in der vorliegenden Übersicht klinische, morphologische und molekulare Kriterien von Azinuszellkarzinomen, Pankreatoblastomen, solid-pseudopapillären Neoplasien und serös-zystischen Neoplasien vorgestellt, anhand derer eine differenzialdiagnostische Einordnung in der Regel leicht möglich ist.
Autres résumés
Type: Publisher
(ger)
Neben dem weitaus häufigsten Pankreastumor, dem duktalen Adenokarzinom des Pankreas, existieren zahlreiche solide und zystische, epitheliale und nichtepitheliale Tumoren im Pankreas, die für sich genommen jeweils selten sind und klinisch ein breites Spektrum von benignen Tumoren bis zu hochaggressiven, metastasierungs- und rezidivfreudigen Neoplasien abdecken. Exemplarisch werden in der vorliegenden Übersicht klinische, morphologische und molekulare Kriterien von Azinuszellkarzinomen, Pankreatoblastomen, solid-pseudopapillären Neoplasien und serös-zystischen Neoplasien vorgestellt, anhand derer eine differenzialdiagnostische Einordnung in der Regel leicht möglich ist.
Identifiants
pubmed: 34402979
doi: 10.1007/s00292-021-00967-0
pii: 10.1007/s00292-021-00967-0
doi:
Types de publication
Journal Article
Review
Langues
ger
Sous-ensembles de citation
IM
Pagination
484-490Informations de copyright
© 2021. Springer Medizin Verlag GmbH, ein Teil von Springer Nature.
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