Prevalence of Germline Variants in a Large Cohort of Japanese Patients with Pheochromocytoma and/or Paraganglioma.

Japanese SDHB SDHD VHL genetics germline variants paraganglioma pheochromocytoma

Journal

Cancers
ISSN: 2072-6694
Titre abrégé: Cancers (Basel)
Pays: Switzerland
ID NLM: 101526829

Informations de publication

Date de publication:
09 Aug 2021
Historique:
received: 25 07 2021
revised: 02 08 2021
accepted: 04 08 2021
entrez: 27 8 2021
pubmed: 28 8 2021
medline: 28 8 2021
Statut: epublish

Résumé

The high incidence of germline variants in pheochromocytoma and paraganglioma (PPGL) has been reported mainly in Europe, but not among Japanese populations in Asia. We aimed to study the prevalence of germline variants in Japanese PPGL patients and the genotype-phenotype correlation. We examined 370 PPGL probands, including 43 patients with family history and/or syndromic presentation and 327 patients with apparently sporadic (AS) presentation. Clinical data and blood samples were collected, and the seven major susceptibility genes (

Identifiants

pubmed: 34439168
pii: cancers13164014
doi: 10.3390/cancers13164014
pmc: PMC8394264
pii:
doi:

Types de publication

Journal Article

Langues

eng

Subventions

Organisme : Japan Society for the Promotion of Science
ID : 201128060B
Organisme : Japan Society for the Promotion of Science
ID : 21591168
Organisme : Japan Society for the Promotion of Science
ID : 23591889
Organisme : Japan Society for the Promotion of Science
ID : 25460671
Organisme : Japan Society for the Promotion of Science
ID : 16K08961
Organisme : Japan Society for the Promotion of Science
ID : 17H04328

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Auteurs

Masato Yonamine (M)

Laboratory of Laboratory/Sports Medicine, Division of Clinical Medicine, Faculty of Medicine, University of Tsukuba, 1-1-1 Tennodai, Tsukuba 305-8577, Ibaraki, Japan.

Koichiro Wasano (K)

Division of Hearing and Balance Research, National Institute of Sensory Organs, National Hospital Organization Tokyo Medical Center, Meguro 152-8902, Tokyo, Japan.

Yuichi Aita (Y)

Department of Endocrinology and Metabolism, Faculty of Medicine, University of Tsukuba, 1-1-1 Tennodai, Tsukuba 305-8577, Ibaraki, Japan.

Takehito Sugasawa (T)

Laboratory of Laboratory/Sports Medicine, Division of Clinical Medicine, Faculty of Medicine, University of Tsukuba, 1-1-1 Tennodai, Tsukuba 305-8577, Ibaraki, Japan.

Katsutoshi Takahashi (K)

Division of Metabolism, Showa General Hospital, 8-1-1 Hanakoganei, Kodaira 187-8510, Tokyo, Japan.

Yasushi Kawakami (Y)

Laboratory of Laboratory/Sports Medicine, Division of Clinical Medicine, Faculty of Medicine, University of Tsukuba, 1-1-1 Tennodai, Tsukuba 305-8577, Ibaraki, Japan.

Hitoshi Shimano (H)

Department of Endocrinology and Metabolism, Faculty of Medicine, University of Tsukuba, 1-1-1 Tennodai, Tsukuba 305-8577, Ibaraki, Japan.

Hiroyuki Nishiyama (H)

Department of Urology, Faculty of Medicine, University of Tsukuba Hospital, 2-1-1 Amakubo, Tsukuba 305-8576, Ibaraki, Japan.

Hisato Hara (H)

Department of Breast and Endocrine Surgery, Faculty of Medicine, University of Tsukuba, 1-1-1 Tennodai, Tsukuba 305-8577, Ibaraki, Japan.

Mitsuhide Naruse (M)

Institute of Clinical Endocrinology and Metabolism, National Hospital Organization Kyoto Medical Center, 1-1 Fukakusamukaihatacho, Fushimi-ku 612-8555, Kyoto, Japan.
Endocrine Center and Clinical Research Center, Ijinkai Takeda General Hospital, 28-1 Ishidamoriminamicho, Fushimi-ku 601-1495, Kyoto, Japan.

Takahiro Okamoto (T)

Department of Breast and Endocrine Surgery, Tokyo Women's Medical University, 8-1 Kawada-cho, Shin-juku-ku 162-8666, Tokyo, Japan.

Tadashi Matsuda (T)

Department of Urology and Andrology, Kansai Medical University, 2-5-1 Shin-machi, Hirakata 573-1010, Osaka, Japan.

Shinji Kosugi (S)

Department of Medical Ethics/Medical Genetics, Kyoto University School of Public Health, Yoshidakonoecho, Sakyo-ku 606-8501, Kyoto, Japan.

Kazuhiko Horiguchi (K)

Division of Endocrinology and Metabolism, Gunma University Graduate School of Medicine, 3-39-15 Showa-machi, Maebashi 371-8511, Gunma, Japan.

Akiyo Tanabe (A)

Department of Diabetes, Endocrinology and Metabolism, Center Hospital of the National Center for Global-Health and Medicine, 1-21-1 Toyama, Shinjuku-ku 162-8855, Tokyo, Japan.

Atsushi Watanabe (A)

Division of Clinical Genetics, Kanazawa University Hospital, 13-1 Takaramachi, Kanazawa 920-8641, Ishikawa, Japan.

Noriko Kimura (N)

Department of Pathology, National Hospital Organization Hakodate National Hospital, 18-16 Kawahara-cho, Hakodate 041-8512, Hokkaido, Japan.

Eijiro Nakamura (E)

Department of Urology, National Cancer Center Hospital, 5-1-1 Tsukiji, Chuo City 104-0045, Tokyo, Japan.

Akihiro Sakurai (A)

Department of Medical Genetics and Genomics, Sapporo Medical University School of Medicine, Minami 1-jo Nishi 17-chome Chuo-ku, Sapporo 060-8556, Hokkaido, Japan.

Kiyoto Shiga (K)

Department of Head and Neck Surgery, Iwate Medical University School of Medicine, 2-1-1 Idaidori, Yaha-ba-cho, Shiwa-gun 028-3695, Iwate, Japan.

Kazuhiro Takekoshi (K)

Laboratory of Laboratory/Sports Medicine, Division of Clinical Medicine, Faculty of Medicine, University of Tsukuba, 1-1-1 Tennodai, Tsukuba 305-8577, Ibaraki, Japan.

Classifications MeSH