Dental phenotype in Crouzon syndrome: A controlled radiographic study in 22 patients.

Craniofacial dysostosis Crouzon syndrome Dental morphology Morphometrics Receptor Fibroblast Growth Factor, type 2 Tooth phenotype

Journal

Archives of oral biology
ISSN: 1879-1506
Titre abrégé: Arch Oral Biol
Pays: England
ID NLM: 0116711

Informations de publication

Date de publication:
Nov 2021
Historique:
received: 28 09 2020
revised: 25 08 2021
accepted: 28 08 2021
pubmed: 10 9 2021
medline: 13 10 2021
entrez: 9 9 2021
Statut: ppublish

Résumé

This retrospective radiographic controlled study investigates the dental phenotype in patients with Crouzon syndrome to determine if differences are observed as suggested by the FGFR2 We assessed dental phenotype using dedicated linear measurements in 22 children with Crouzon syndrome and compared tooth morphology in both primary and permanent dentitions to an age-matched control group. Descriptive statistics were performed with "Sex" and "Age" as covariates for the permanent tooth models and "Sex" only for the primary tooth models, to take into account potential confounding factors. We showed that permanent but not primary tooth dimensions were globally reduced in Crouzon syndrome, without microdontia. In permanent dentition, crown height, mesiodistal and faciolingual cervical diameters were reduced by 6.3%, 5.7% and 5.5% respectively (p < 0.05). Our results underline the implication of Fibroblast Growth Factor Receptor 2 (FGFR2) in dental development of humans and contribute to support FGFR2

Identifiants

pubmed: 34500259
pii: S0003-9969(21)00216-8
doi: 10.1016/j.archoralbio.2021.105253
pii:
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

105253

Informations de copyright

Copyright © 2021 Elsevier Ltd. All rights reserved.

Auteurs

Ludovic Sicard (L)

UFR d'Odontologie Garancière, Université de Paris, 5 rue de Garancière, 75006 Paris, France; Service de Chirurgie Maxillo-Faciale et Chirurgie Plastique, Hôpital Necker - Enfants Malades, Assistance Publique - Hôpitaux de Paris; Centre de Référence Fentes et Malformations Faciales MAFACE, Filière Maladies Rares TeteCou; Université de Paris, Paris, France. Electronic address: ludovic.sicard@aphp.fr.

Quentin Hennocq (Q)

Service de Chirurgie Maxillo-Faciale et Chirurgie Plastique, Hôpital Necker - Enfants Malades, Assistance Publique - Hôpitaux de Paris; Centre de Référence Fentes et Malformations Faciales MAFACE, Filière Maladies Rares TeteCou; Université de Paris, Paris, France.

Giovanna Paternoster (G)

Unité Fonctionnelle de Chirurgie Craniofaciale, Service de Neurochirurgie, Hôpital Necker - Enfants Malades, Assistance Publique - Hôpitaux de Paris; Centre de Référence Craniosténoses et Malformations Craniofaciales CRANIOST, Filière Maladies Rares TeteCou; Université de Paris, Paris, France.

Eric Arnaud (E)

Unité Fonctionnelle de Chirurgie Craniofaciale, Service de Neurochirurgie, Hôpital Necker - Enfants Malades, Assistance Publique - Hôpitaux de Paris; Centre de Référence Craniosténoses et Malformations Craniofaciales CRANIOST, Filière Maladies Rares TeteCou; Université de Paris, Paris, France.

Muriel de la Dure-Molla (M)

UFR d'Odontologie Garancière, Université de Paris, 5 rue de Garancière, 75006 Paris, France.

Roman Hossein Khonsari (RH)

Service de Chirurgie Maxillo-Faciale et Chirurgie Plastique, Hôpital Necker - Enfants Malades, Assistance Publique - Hôpitaux de Paris; Centre de Référence Fentes et Malformations Faciales MAFACE, Filière Maladies Rares TeteCou; Université de Paris, Paris, France; Unité Fonctionnelle de Chirurgie Craniofaciale, Service de Neurochirurgie, Hôpital Necker - Enfants Malades, Assistance Publique - Hôpitaux de Paris; Centre de Référence Craniosténoses et Malformations Craniofaciales CRANIOST, Filière Maladies Rares TeteCou; Université de Paris, Paris, France.

Articles similaires

[Redispensing of expensive oral anticancer medicines: a practical application].

Lisanne N van Merendonk, Kübra Akgöl, Bastiaan Nuijen
1.00
Humans Antineoplastic Agents Administration, Oral Drug Costs Counterfeit Drugs

Smoking Cessation and Incident Cardiovascular Disease.

Jun Hwan Cho, Seung Yong Shin, Hoseob Kim et al.
1.00
Humans Male Smoking Cessation Cardiovascular Diseases Female
Humans United States Aged Cross-Sectional Studies Medicare Part C
1.00
Humans Yoga Low Back Pain Female Male

Classifications MeSH