IgG4-related pachymeningitis and mastoiditis, associated with cerebral venous thrombosis: A case report.
Abducens Nerve Diseases
/ etiology
Adrenal Cortex Hormones
/ therapeutic use
Adult
Dabigatran
/ therapeutic use
Female
Humans
Immunoglobulin G4-Related Disease
/ blood
Lateral Sinus Thrombosis
/ etiology
Lung
/ diagnostic imaging
Magnetic Resonance Imaging
Mastoidectomy
Mastoiditis
/ diagnostic imaging
Meningitis
/ diagnostic imaging
Neuroimaging
Rituximab
/ therapeutic use
Thrombophilia
/ drug therapy
Tomography, X-Ray Computed
Venous Thrombosis
/ etiology
Cerebral venous thrombosis
Classification criteria
Clinico-pathologic confirmation
IgG4-related disease
Inflammatory pseudotumor
Skull base
Journal
Journal of neuroimmunology
ISSN: 1872-8421
Titre abrégé: J Neuroimmunol
Pays: Netherlands
ID NLM: 8109498
Informations de publication
Date de publication:
15 11 2021
15 11 2021
Historique:
received:
25
05
2021
revised:
12
08
2021
accepted:
05
09
2021
pubmed:
14
9
2021
medline:
8
1
2022
entrez:
13
9
2021
Statut:
ppublish
Résumé
IgG4-related disease (IgG4-RD) is a multisystem fibroinflammatory condition; this can be a challenging diagnosis that requires clinico-pathologic correlation. We report a young woman, presenting with cranial nerve palsy. The work-up revealed pachymeningitis, cerebral venous thrombosis (CVT), and a destructive lesion in the mastoid. We diagnosed IgG4-RD through mastoidectomy. Thus, a biopsy of asymptomatic, infrequently affected organs, like the mastoid, can meet all histopathological criteria. In neuro-meningeal presentations, CVT may be secondary to the local inflammatory environment of pachymeningitis. Since our patient had a deep vein thrombosis one year prior, we discuss a possible higher risk of thrombosis in IgG4-RD patients.
Identifiants
pubmed: 34517153
pii: S0165-5728(21)00244-7
doi: 10.1016/j.jneuroim.2021.577717
pii:
doi:
Substances chimiques
Adrenal Cortex Hormones
0
Rituximab
4F4X42SYQ6
Dabigatran
I0VM4M70GC
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
577717Informations de copyright
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