Pulmonary veno-occlusive disease in childhood-a rare disease not to be missed.

Pulmonary hypertension ground-glass opacities pulmonary edema pulmonary veno-occlusive disease (PVOD)

Journal

Cardiovascular diagnosis and therapy
ISSN: 2223-3652
Titre abrégé: Cardiovasc Diagn Ther
Pays: China
ID NLM: 101601613

Informations de publication

Date de publication:
Aug 2021
Historique:
received: 04 03 2020
accepted: 27 05 2020
entrez: 16 9 2021
pubmed: 17 9 2021
medline: 17 9 2021
Statut: ppublish

Résumé

Pulmonary veno-occlusive disease (PVOD) is a rare disease leading to pulmonary hypertension and potentially death related to right heart failure and/or respiratory insufficiency. Clinical symptoms are heterogenous and nonspecific: fatigue, decreased exercise tolerance, shortness of breath on exertion, cough, dizziness, chest pain with exercise, palpitations, syncope, as well as nonspecific symptoms such as headache, poor appetite, pallor or perioral cyanosis. Mutations in the

Identifiants

pubmed: 34527533
doi: 10.21037/cdt-20-320
pii: cdt-11-04-1070
pmc: PMC8410504
doi:

Types de publication

Journal Article Review

Langues

eng

Pagination

1070-1079

Informations de copyright

2021 Cardiovascular Diagnosis and Therapy. All rights reserved.

Déclaration de conflit d'intérêts

Conflicts of Interest: Both authors have completed the ICMJE uniform disclosure form (available at http://dx.doi.org/10.21037/cdt-20-320). The series “Pediatric Pulmonary Hypertension” was commissioned by the editorial office without any funding or sponsorship. The authors have no other conflicts of interest to declare.

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Auteurs

Marc Pfluger (M)

Department of Pediatrics, Children's Hospital, Inselspital, University of Berne, Berne, Switzerland.

Tilman Humpl (T)

Department of Pediatrics, Children's Hospital, Inselspital, University of Berne, Berne, Switzerland.

Classifications MeSH