Infantile Scimitar Syndrome With Contralateral Pulmonary Vein Stenosis and Refractory Pulmonary Hypertension.

cardiac catheterization infantile scimitar syndrome pulmonary hypertension pulmonary vein stenosis scimitar syndrome

Journal

Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737

Informations de publication

Date de publication:
Aug 2021
Historique:
accepted: 15 08 2021
entrez: 20 9 2021
pubmed: 21 9 2021
medline: 21 9 2021
Statut: epublish

Résumé

Infantile scimitar syndrome is associated with pulmonary hypertension which can be difficult to manage. We present a three-month-old infant with scimitar syndrome, who eventually developed refractory pulmonary hypertension, posing a significant management challenge. Further workup demonstrated contralateral pulmonary vein stenosis, which is rarely described in scimitar syndrome. Our index case highlights the importance of follow-up cardiac catheterizations in these patients with severe pulmonary hypertension.

Identifiants

pubmed: 34540431
doi: 10.7759/cureus.17203
pmc: PMC8439397
doi:

Types de publication

Case Reports

Langues

eng

Pagination

e17203

Informations de copyright

Copyright © 2021, Buysse et al.

Déclaration de conflit d'intérêts

The authors have declared that no competing interests exist.

Références

Am Heart J. 2013 May;165(5):770-7
pubmed: 23622914
Braz J Cardiovasc Surg. 2021 Feb 01;36(1):133-136
pubmed: 33594868
Circulation. 2010 Sep 21;122(12):1159-66
pubmed: 20823387
J Am Coll Cardiol. 1993 Sep;22(3):873-82
pubmed: 8354827
Ann Pediatr Cardiol. 2014 Jan;7(1):29-33
pubmed: 24701082
Ann Thorac Surg. 1999 Jan;67(1):154-9; discussion 160
pubmed: 10086541
Pediatr Cardiol. 2010 May;31(4):550-2
pubmed: 20054529
Circulation. 2015 Nov 24;132(21):2037-99
pubmed: 26534956

Auteurs

Janelle Buysse (J)

Pediatric Cardiology, University of Iowa Stead Family Children's Hospital, Iowa City, USA.

Ramya Deepthi Billa (RD)

Division of Critical Care Medicine, University of Iowa Stead Family Children's Hospital, Iowa City, USA.

Daniel McLennan (D)

Pediatric Cardiology, University of Iowa Stead Family Children's Hospital, Iowa City, USA.

Ravi Ashwath (R)

Pediatric Cardiology, University of Iowa Stead Family Children's Hospital, Iowa City, USA.

Aditya Badheka (A)

Pediatrics, University of Iowa Hospitals and Clinics, Iowa City, USA.
Pediatrics, University of Iowa Stead Family Children's Hospital, Iowa City, USA.

Madhuradhar Chegondi (M)

Pediatrics, University of Iowa Stead Family Children's Hospital, Iowa City, USA.

Classifications MeSH