Global geographic differences in healthcare utilization for sickle cell disease pain crises in the CASiRe cohort.


Journal

Blood cells, molecules & diseases
ISSN: 1096-0961
Titre abrégé: Blood Cells Mol Dis
Pays: United States
ID NLM: 9509932

Informations de publication

Date de publication:
12 2021
Historique:
received: 13 07 2021
revised: 13 09 2021
accepted: 15 09 2021
pubmed: 27 9 2021
medline: 5 2 2022
entrez: 26 9 2021
Statut: ppublish

Résumé

Sickle cell disease (SCD) is characterized by frequent, unpredictable pain episodes and other vaso-occlusive crises (VOCs) leading to significant healthcare utilization. VOC frequency is often an endpoint in clinical trials investigating novel therapies for this devastating disease. The Consortium for the Advancement of Sickle Cell Research (CASiRe) is an international collaboration investigating clinical severity in SCD using a validated questionnaire and medical chart review standardized across four countries (United States, United Kingdom, Italy and Ghana). This study, focused on pain crisis incidence and healthcare utilization, included 868 patients, equally represented according to age and gender. HgbSS was the most common genotype. Patients from Ghana used the Emergency Room/Day Hospital for pain more frequently (annualized mean 2.01) than patients from other regions (annualized mean 1.56 U.S.; 1.09 U.K.; 0.02 Italy), while U.K. patients were hospitalized for pain more often (annualized mean: U.K. 2.98) than patients in other regions (annualized mean 1.98 U.S.; 1.18 Ghana; Italy 0.54). Italy's hospitalization rate for pain (annualized mean: 0.57) was nearly 20 times greater than its emergency room/day hospital only visits for pain (annualized mean: 0.03). When categorized by genotype and age, similar results were seen. Geographic differences in pain crisis frequency and healthcare utilization may correlate with variable organization of healthcare systems among countries and should be considered regarding trial design, endpoints, and analysis of results when investigating novel agents for clinical benefit.

Sections du résumé

BACKGROUND
Sickle cell disease (SCD) is characterized by frequent, unpredictable pain episodes and other vaso-occlusive crises (VOCs) leading to significant healthcare utilization. VOC frequency is often an endpoint in clinical trials investigating novel therapies for this devastating disease.
PROCEDURE
The Consortium for the Advancement of Sickle Cell Research (CASiRe) is an international collaboration investigating clinical severity in SCD using a validated questionnaire and medical chart review standardized across four countries (United States, United Kingdom, Italy and Ghana).
RESULTS
This study, focused on pain crisis incidence and healthcare utilization, included 868 patients, equally represented according to age and gender. HgbSS was the most common genotype. Patients from Ghana used the Emergency Room/Day Hospital for pain more frequently (annualized mean 2.01) than patients from other regions (annualized mean 1.56 U.S.; 1.09 U.K.; 0.02 Italy), while U.K. patients were hospitalized for pain more often (annualized mean: U.K. 2.98) than patients in other regions (annualized mean 1.98 U.S.; 1.18 Ghana; Italy 0.54). Italy's hospitalization rate for pain (annualized mean: 0.57) was nearly 20 times greater than its emergency room/day hospital only visits for pain (annualized mean: 0.03). When categorized by genotype and age, similar results were seen.
CONCLUSIONS
Geographic differences in pain crisis frequency and healthcare utilization may correlate with variable organization of healthcare systems among countries and should be considered regarding trial design, endpoints, and analysis of results when investigating novel agents for clinical benefit.

Identifiants

pubmed: 34564050
pii: S1079-9796(21)00078-4
doi: 10.1016/j.bcmd.2021.102612
pmc: PMC8643307
mid: NIHMS1743333
pii:
doi:

Types de publication

Journal Article Research Support, N.I.H., Extramural

Langues

eng

Sous-ensembles de citation

IM

Pagination

102612

Subventions

Organisme : NIMHD NIH HHS
ID : T37 MD001425
Pays : United States

Informations de copyright

Copyright © 2021 Elsevier Inc. All rights reserved.

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Auteurs

Crawford Strunk (C)

Department of Pediatric Hematology/Oncology, ProMedica Russell J. Ebeid Children's Hospital, Toledo, OH, USA. Electronic address: Crawford.Strunk@ProMedica.org.

Immacolata Tartaglione (I)

Department of Women, Child and General and Specialized Surgery, University of Campania "Luigi Vanvitelli", Naples, Italy.

Connie M Piccone (CM)

Pediatric Hematology, Carle Foundation Hospital, Urbana, IL, USA.

Raffaella Colombatti (R)

Clinic of Pediatric Hematology Oncology, Department of Women's and Child Health, Azienda Ospedaliera-Università di Padova, Padova, Italy.

Biree Andemariam (B)

New England Sickle Cell Institute, Division of Hematology-Oncology, Neag Comprehensive Cancer Center, UCONN Health, University of Connecticut, Farmington, CT, USA.

Deepa Manwani (D)

Department of Pediatrics, Albert Einstein College of Medicine, Children's Hospital at Montefiore, Bronx, NY, USA.

Ashya Smith (A)

Division of Pediatric Hematology/Oncology, University of Michigan, Ann Arbor, MI, USA.

Haikel Haile (H)

Division of Pediatric Hematology/Oncology, University of Michigan, Ann Arbor, MI, USA.

Esther Kim (E)

Division of Pediatric Hematology/Oncology, University of Michigan, Ann Arbor, MI, USA.

Samuel Wilson (S)

Division of Pediatric Hematology/Oncology, University of Michigan, Ann Arbor, MI, USA.

Eugenia Vicky Asare (EV)

Ghana Institute of Clinical Genetics, Korle Bu Teaching Hospital, Accra, Ghana.

Angela Rivers (A)

UCSF Benioff Children's Hospital Oakland, Oakland, CA, USA.

Fatimah Farooq (F)

Division of Pediatric Hematology/Oncology, University of Michigan, Ann Arbor, MI, USA.

Rebekah Urbonya (R)

Division of Pediatric Hematology/Oncology, University of Michigan, Ann Arbor, MI, USA.

Donna Boruchov (D)

Department of Child Health, Korle Bu Teaching Hospital, Accra, Ghana.

Gifty Dankwah Boatemaa (GD)

Department of Physiology, University of Ghana Medical School, University of Ghana, Accra, Ghana.

Silverio Perrotta (S)

Department of Women, Child and General and Specialized Surgery, University of Campania "Luigi Vanvitelli", Naples, Italy.

Ivy Ekem (I)

Ghana Institute of Clinical Genetics, Korle Bu Teaching Hospital, Accra, Ghana.

Laura Sainati (L)

Clinic of Pediatric Hematology Oncology, Department of Women's and Child Health, Azienda Ospedaliera-Università di Padova, Padova, Italy.

Sudha Rao (S)

Department of Child Health, Korle Bu Teaching Hospital, Accra, Ghana.

William Zempsky (W)

Division of Pain and Palliative Care, Department of Pediatrics, University of Connecticut School of Medicine, Connecticut Children's Medical Center, Hartford, CT, USA.

Fredericka Sey (F)

Ghana Institute of Clinical Genetics, Korle Bu Teaching Hospital, Accra, Ghana.

Charles Antwi-Boasiako (C)

Department of Physiology, University of Ghana Medical School, University of Ghana, Accra, Ghana; Ghana Institute of Clinical Genetics, Korle Bu Teaching Hospital, Accra, Ghana.

Catherine Segbefia (C)

Department of Child Health, Korle Bu Teaching Hospital, Accra, Ghana; Department of Child Health, University of Ghana Medical School, University of Ghana, Accra, Ghana.

Baba Inusa (B)

Department of Pediatric Haematology, Evelina Children's Hospital, Guy's and St. Thomas NHS Trust, London, UK.

Andrew D Campbell (AD)

Division of Pediatric Hematology/Oncology, University of Michigan, Ann Arbor, MI, USA; Department of Pediatrics, Divison of Hematology, Children's National Hospital, George Washington University School of Medicine Health Sciences, Washington, DC, USA.

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