Giant Pulmonary Artery Thrombotic Material, Due to Chronic Thromboembolic Pulmonary Hypertension, Mimics Pulmonary Artery Sarcoma.
chronic thromboembolic pulmonary hypertension
pulmonary artery sarcoma
pulmonary endarterectomy
Journal
Medicina (Kaunas, Lithuania)
ISSN: 1648-9144
Titre abrégé: Medicina (Kaunas)
Pays: Switzerland
ID NLM: 9425208
Informations de publication
Date de publication:
20 Sep 2021
20 Sep 2021
Historique:
received:
13
08
2021
revised:
07
09
2021
accepted:
16
09
2021
entrez:
28
9
2021
pubmed:
29
9
2021
medline:
30
9
2021
Statut:
epublish
Résumé
In this article, we present the case of a 38-year-old female who suffered from serious respiratory distress. After an extensive pulmonary artery imaging diagnostic work-up (CTPA, MRA and PET), we were unable to differentiate between chronic thromboembolic pulmonary hypertension (CTEPH) vs. pulmonary artery sarcoma (PAS) due to extensive filling defects and extraluminal findings. Although surgery was postponed for nine months due to the COVID-19 pandemic, CTEPH diagnosis, due to a high-thrombus burden, was finally confirmed after pulmonary endarterectomy (PEA). Conclusively, imaging findings of rare cases of CTEPH might mimic PAS and the surgical removal of the lesion are both needed for a final diagnosis.
Identifiants
pubmed: 34577914
pii: medicina57090992
doi: 10.3390/medicina57090992
pmc: PMC8465601
pii:
doi:
Types de publication
Case Reports
Langues
eng
Sous-ensembles de citation
IM
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