The immune landscape of SARS-CoV-2-associated Multisystem Inflammatory Syndrome in Children (MIS-C) from acute disease to recovery.

Genomics Immune response Immune system disorder Immunology

Journal

iScience
ISSN: 2589-0042
Titre abrégé: iScience
Pays: United States
ID NLM: 101724038

Informations de publication

Date de publication:
19 Nov 2021
Historique:
received: 12 07 2021
revised: 10 09 2021
accepted: 26 09 2021
pubmed: 12 10 2021
medline: 12 10 2021
entrez: 11 10 2021
Statut: ppublish

Résumé

Multisystem inflammatory syndrome in children (MIS-C) is a life-threatening disease occurring several weeks after severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2) infection. Deep immune profiling showed acute MIS-C patients had highly activated neutrophils, classical monocytes and memory CD8+ T-cells, with increased frequencies of B-cell plasmablasts and double-negative B-cells. Post treatment samples from the same patients, taken during symptom resolution, identified recovery-associated immune features including increased monocyte CD163 levels, emergence of a new population of immature neutrophils and, in some patients, transiently increased plasma arginase. Plasma profiling identified multiple features shared by MIS-C, Kawasaki Disease and COVID-19 and that therapeutic inhibition of IL-6 may be preferable to IL-1 or TNF-α. We identified several potential mechanisms of action for IVIG, the most commonly used drug to treat MIS-C. Finally, we showed systemic complement activation with high plasma C5b-9 levels is common in MIS-C suggesting complement inhibitors could be used to treat the disease.

Identifiants

pubmed: 34632327
doi: 10.1016/j.isci.2021.103215
pii: S2589-0042(21)01183-4
pmc: PMC8487319
doi:

Types de publication

Journal Article

Langues

eng

Pagination

103215

Subventions

Organisme : HCRW_
ID : HCRW_HF-19-1595
Pays : United Kingdom

Informations de copyright

© 2021 The Authors.

Déclaration de conflit d'intérêts

The authors declare no competing interests.

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Auteurs

Eleni Syrimi (E)

Institute of Immunology and Immunotherapy, University of Birmingham, B15 2TT Birmingham, UK.

Eanna Fennell (E)

Health Research Institute and the Bernal Institute, University of Limerick, Limerick, Ireland.

Alex Richter (A)

Clinical Immunology Service, Institute of Immunology and Immunotherapy, University of Birmingham, B15 2TT Birmingham, UK.

Pavle Vrljicak (P)

Warwick Medical School, University of Warwick, Coventry, UK.

Richard Stark (R)

Bioinformatics Research Technology Platform, University of Warwick, Coventry, UK.

Sascha Ott (S)

Warwick Medical School, University of Warwick, Coventry, UK.
Bioinformatics Research Technology Platform, University of Warwick, Coventry, UK.

Paul G Murray (PG)

Institute of Immunology and Immunotherapy, University of Birmingham, B15 2TT Birmingham, UK.
Health Research Institute and the Bernal Institute, University of Limerick, Limerick, Ireland.

Eslam Al-Abadi (E)

Birmingham Women's and Children's NHS Foundation Trust, Birmingham, UK.

Ashish Chikermane (A)

Birmingham Women's and Children's NHS Foundation Trust, Birmingham, UK.

Pamela Dawson (P)

Birmingham Women's and Children's NHS Foundation Trust, Birmingham, UK.

Scott Hackett (S)

Heartlands Hospital, University Hospitals Birmingham NHS Foundation Trust, Birmingham, UK.

Deepthi Jyothish (D)

Birmingham Women's and Children's NHS Foundation Trust, Birmingham, UK.

Hari Krishnan Kanthimathinathan (HK)

Birmingham Women's and Children's NHS Foundation Trust, Birmingham, UK.

Sean Monaghan (S)

Birmingham Women's and Children's NHS Foundation Trust, Birmingham, UK.

Prasad Nagakumar (P)

Birmingham Women's and Children's NHS Foundation Trust, Birmingham, UK.
Institute of Inflammation and Ageing, University of Birmingham, Birmingham, UK.

Barnaby R Scholefield (BR)

Birmingham Women's and Children's NHS Foundation Trust, Birmingham, UK.
Institute of Inflammation and Ageing, University of Birmingham, Birmingham, UK.

Steven Welch (S)

Heartlands Hospital, University Hospitals Birmingham NHS Foundation Trust, Birmingham, UK.

Naeem Khan (N)

Clinical Immunology Service, Institute of Immunology and Immunotherapy, University of Birmingham, B15 2TT Birmingham, UK.

Sian Faustini (S)

Clinical Immunology Service, Institute of Immunology and Immunotherapy, University of Birmingham, B15 2TT Birmingham, UK.

Kate Davies (K)

Systems Immunity Research Institute, School of Medicine, Cardiff University, Cardiff, UK.

Wioleta M Zelek (WM)

Systems Immunity Research Institute, School of Medicine, Cardiff University, Cardiff, UK.

Pamela Kearns (P)

NIHR Birmingham Biomedical Research Centre and Institute of Cancer and Genomic Sciences, University of Birmingham, Birmingham, UK.

Graham S Taylor (GS)

Institute of Immunology and Immunotherapy, University of Birmingham, B15 2TT Birmingham, UK.

Classifications MeSH