Intradural Extramedullary Solitary Fibrous Tumor of the Thoracic Spinal Cord.
extramedullary
hemangiopericytoma
intradural
neoplasm
primary tumor
solitary fibrous tumor
thoracic spinal cord
Journal
Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737
Informations de publication
Date de publication:
Oct 2021
Oct 2021
Historique:
accepted:
08
10
2021
entrez:
12
11
2021
pubmed:
13
11
2021
medline:
13
11
2021
Statut:
epublish
Résumé
Solitary fibrous tumors (SFTs) are rare soft tissue neoplasms that can impact the central nervous system (CNS). SFTs comprise <1% of all primary CNS tumors. Here, we describe a rare case of intradural, extramedullary SFT arising within the thoracic spine that was treated with surgical resection. Histological features were evaluated and revealed a highly cellular tumor with positive expression of BCL2, CD34, CD99, and STAT6 proteins that are consistent with a diagnosis of SFT. We discuss the use of surgical intervention for long-term disease control of spinal SFT and evaluate the role of postoperative radiation therapy in management strategies. Lastly, we review the literature reports of intradural, extramedullary SFTs in the thoracic spine. The importance of molecular characterization by histopathology to properly determine diagnosis and prognosis is emphasized.
Identifiants
pubmed: 34765368
doi: 10.7759/cureus.18613
pmc: PMC8572645
doi:
Types de publication
Case Reports
Langues
eng
Pagination
e18613Informations de copyright
Copyright © 2021, Olmsted et al.
Déclaration de conflit d'intérêts
The authors have declared that no competing interests exist.
Références
Acta Oncol. 2021 Jan;60(1):35-41
pubmed: 32988268
Neurosurgery. 2013 Jan;72(1):16-24; discussion 24
pubmed: 23147785
J Neurooncol. 2019 Jul;143(3):457-464
pubmed: 31054100
Radiol Case Rep. 2020 Apr 07;15(6):709-711
pubmed: 32280404
Mod Pathol. 2017 Oct;30(10):1433-1442
pubmed: 28731041
J Neuropathol Exp Neurol. 2016 Mar;75(3):263-71
pubmed: 26883114
Spinal Cord. 2001 Jan;39(1):57-60
pubmed: 11224018
Eur Spine J. 2015 May;24 Suppl 4:S606-13
pubmed: 25662907
Neurosurgery. 1997 Apr;40(4):844-7; discussion 847
pubmed: 9092861
Cancer. 2004 Apr 1;100(7):1491-7
pubmed: 15042684
Neurosurgery. 2007 Dec;61(6):E1336-7; discussion E1337
pubmed: 18162866
Chin Med J (Engl). 2007 Jan 20;120(2):115-9
pubmed: 17335652
Folia Neuropathol. 2018;56(2):151-157
pubmed: 30509035
Spine (Phila Pa 1976). 2011 Nov 1;36(23):E1534-9
pubmed: 21857403
Biomed Res Int. 2020 Nov 2;2020:2468320
pubmed: 33204688
Eur Spine J. 2013 May;22 Suppl 3:S450-9
pubmed: 23291785
Case Rep Orthop. 2019 Nov 22;2019:3926903
pubmed: 31885980
Neurosurgery. 2005 Jul;57(1):E195; discussion E195
pubmed: 15987560
Asian Spine J. 2015 Aug;9(4):522-8
pubmed: 26240709
Nat Genet. 2013 Feb;45(2):131-2
pubmed: 23313954
J Neurol Surg B Skull Base. 2017 Aug;78(4):324-330
pubmed: 28725519
J Neurosurg. 2018 Dec 1;129(6):1384-1396
pubmed: 29372881
Acta Neuropathol. 2019 Feb;137(2):307-319
pubmed: 30584643
Neurosurg Rev. 2021 Jun;44(3):1299-1312
pubmed: 32556679
Eur Spine J. 2018 Apr;27(4):891-901
pubmed: 29127512
World Neurosurg. 2017 Aug;104:318-329
pubmed: 28512044
J Clin Neurosci. 2013 Feb;20(2):317-9
pubmed: 23153873
J Neurosurg. 2010 Aug;113(2):333-9
pubmed: 20367074
Ann Diagn Pathol. 2004 Oct;8(5):268-75
pubmed: 15494932
J Neurooncol. 2018 May;137(3):567-573
pubmed: 29327171
Neurology. 1965 Jul;15:649-53
pubmed: 14306325
Spine J. 2011 Jul;11(7):e9-e14
pubmed: 21641873
Global Spine J. 2021 Mar 11;:2192568221994799
pubmed: 33691508
J Neurosurg. 2000 Apr;92(2 Suppl):217-20
pubmed: 10763696
No Shinkei Geka. 2012 Apr;40(4):351-7
pubmed: 22466235
J Surg Case Rep. 2017 Jul 04;2017(7):rjx121
pubmed: 28690777
Neurocirugia (Astur : Engl Ed). 2020 Jan - Feb;31(1):14-23
pubmed: 31351895
Childs Nerv Syst. 2015 Jan;31(1):173-5
pubmed: 25059986
Neuro Oncol. 2021 Aug 2;23(8):1231-1251
pubmed: 34185076
J Chin Med Assoc. 2009 Oct;72(10):536-41
pubmed: 19837649
Mod Pathol. 2012 Sep;25(9):1298-306
pubmed: 22575866
Cancer Res Treat. 2021 Mar 24;:
pubmed: 33781051
Acta Neuropathol. 2016 Jun;131(6):803-20
pubmed: 27157931