Coronary artery patch augmentation for congenital left coronary ostial stenosis in Williams syndrome.


Journal

Multimedia manual of cardiothoracic surgery : MMCTS
ISSN: 1813-9175
Titre abrégé: Multimed Man Cardiothorac Surg
Pays: England
ID NLM: 101495626

Informations de publication

Date de publication:
20 Aug 2021
Historique:
entrez: 12 11 2021
pubmed: 13 11 2021
medline: 26 11 2021
Statut: epublish

Résumé

Left coronary ostial stenosis, which is associated with sudden death, occasionally occurs in individuals with Williams syndrome. However, surgical methods that provide reliable long-term revascularization remain unknown among infants and young children with coronary ostial stenosis. We describe the case of an 18-month-old boy with Williams syndrome who presented with cardiogenic shock due to left coronary ostial stenosis. We performed patch augmentation of the left coronary ostium using glutaraldehyde-treated autologous pericardium. At the last follow-up, the patient was well without any adverse events or myocardial ischemia.

Identifiants

pubmed: 34767699
doi: 10.1510/mmcts.2021.062
doi:

Types de publication

Case Reports Video-Audio Media

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© The Author 2021. Published by MMCTS on behalf of the European Association for Cardio-Thoracic Surgery. All rights reserved.

Auteurs

Kunihiko Joo (K)

Cardiovascular Surgery, Japan Community Health Care Organization, Kyushu Hospital, Fukuoka, Japan.

Yoshie Ochiai (Y)

Cardiovascular Surgery, Japan Community Health Care Organization, Kyushu Hospital, Fukuoka, Japan.

Koji Okamoto (K)

Cardiovascular Surgery, Japan Community Health Care Organization, Kyushu Hospital, Fukuoka, Japan.

Yoshiyuki Yamashita (Y)

Cardiovascular Surgery, Japan Community Health Care Organization, Kyushu Hospital, Fukuoka, Japan.

Jun Muneuchi (J)

Pediatric Cardiology, Japan Community Health Care Organization, Kyushu Hospital, Fukuoka, Japan.

Shigehiko Tokunaga (S)

Cardiovascular Surgery, Japan Community Health Care Organization, Kyushu Hospital, Fukuoka, Japan.

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Classifications MeSH