Screening of Neonatal UK Dried Blood Spots Using a Duplex SMN1 Screening Assay.

NBS SMA SMN1 dried blood spot newborn screening spinal muscular atrophy

Journal

International journal of neonatal screening
ISSN: 2409-515X
Titre abrégé: Int J Neonatal Screen
Pays: Switzerland
ID NLM: 101665400

Informations de publication

Date de publication:
26 Oct 2021
Historique:
received: 06 09 2021
revised: 21 10 2021
accepted: 21 10 2021
entrez: 29 11 2021
pubmed: 30 11 2021
medline: 30 11 2021
Statut: epublish

Résumé

Spinal muscular atrophy (SMA) is an autosomal inherited neuromuscular genetic disease caused, in 95% of cases, by homozygous deletions involving the

Identifiants

pubmed: 34842601
pii: ijns7040069
doi: 10.3390/ijns7040069
pmc: PMC8629004
pii:
doi:

Types de publication

Journal Article

Langues

eng

Références

Clin Lab Med. 2020 Sep;40(3):357-367
pubmed: 32718505
J Clin Immunol. 2014 Apr;34(3):323-30
pubmed: 24668299
Orphanet J Rare Dis. 2017 Jul 4;12(1):124
pubmed: 28676062
Genet Med. 2018 Jun;20(6):608-613
pubmed: 29758563
J Neurol. 2017 Jul;264(7):1465-1473
pubmed: 28634652
J Neuromuscul Dis. 2019;6(4):503-515
pubmed: 31594245
J Pediatr. 2017 Nov;190:124-129.e1
pubmed: 28711173
Int J Neonatal Screen. 2019 Nov 02;5(4):39
pubmed: 33072998
Neuromuscul Disord. 2019 May;29(5):343-349
pubmed: 31030938

Auteurs

Stuart P Adams (SP)

SIHMDS-Haematology, Camelia Botnar Labs, Great Ormond Street Hospital for Children, London WC1N 3JH, UK.
Infection, Immunity and Inflammation Section, UCL Great Ormond Street Institute of Child Health, London WC1N 1EH, UK.

Emma Gravett (E)

SIHMDS-Haematology, Camelia Botnar Labs, Great Ormond Street Hospital for Children, London WC1N 3JH, UK.

Natalie Kent (N)

SIHMDS-Haematology, Camelia Botnar Labs, Great Ormond Street Hospital for Children, London WC1N 3JH, UK.

Susanne Kricke (S)

SIHMDS-Haematology, Camelia Botnar Labs, Great Ormond Street Hospital for Children, London WC1N 3JH, UK.

Adeboye Ifederu (A)

Newborn Screening Unit, Camelia Botnar Labs, Great Ormond Street Hospital for Children, London WC1N 3JH, UK.

Mariacristina Scoto (M)

Developmental Neurosciences Research & Teaching Department, Molecular Neurosciences, Dubowitz Neuromuscular Unit, UCL Great Ormond Street Institute of Child Health, London WC1N 1EH, UK.
The Dubowitz Neuromuscular Centre, Great Ormond Street Hospital, London WC1N 1EH, UK.

Salma Samsuddin (S)

Developmental Neurosciences Research & Teaching Department, Molecular Neurosciences, Dubowitz Neuromuscular Unit, UCL Great Ormond Street Institute of Child Health, London WC1N 1EH, UK.

Francesco Muntoni (F)

Developmental Neurosciences Research & Teaching Department, Molecular Neurosciences, Dubowitz Neuromuscular Unit, UCL Great Ormond Street Institute of Child Health, London WC1N 1EH, UK.

Classifications MeSH