Atypical Presentation of Testicular Adrenal Rest Tumor (TART) Leading to Bilateral Partial Orchiectomy in a 31-Year-Old Adult Revealing Primary Adrenal Insufficiency with


Journal

Case reports in endocrinology
ISSN: 2090-6501
Titre abrégé: Case Rep Endocrinol
Pays: United States
ID NLM: 101576457

Informations de publication

Date de publication:
2021
Historique:
received: 27 09 2021
revised: 12 12 2021
accepted: 15 12 2021
entrez: 3 1 2022
pubmed: 4 1 2022
medline: 4 1 2022
Statut: epublish

Résumé

Adrenogenital syndrome is commonly associated with a deficiency in 21-hydroxylase but can be present in other rare enzymatic blocks. We report here the case of a 31-year-old man who presented with bilateral painful testicle lesions leading to bilateral partial orchiectomy as they were suspected for malignancy. These lesions were finally identified as benign testicle adrenal rest tumors (TARTs), and the patient was actually belatedly diagnosed with primary adrenal insufficiency due to 2 mutations of the

Identifiants

pubmed: 34976419
doi: 10.1155/2021/5889007
pmc: PMC8718273
doi:

Types de publication

Case Reports

Langues

eng

Pagination

5889007

Informations de copyright

Copyright © 2021 Cyril Garcia et al.

Déclaration de conflit d'intérêts

The authors declare that they have no conflicts of interest.

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Auteurs

Cyril Garcia (C)

Hôpital d'Instruction des Armées BEGIN, Service d'endocrinologie, 69 avenue de Paris, Saint-Mande 94160, France.

Marie Dusaud (M)

Hôpital d'Instruction des Armées BEGIN, Service d'urologie, 69 avenue de Paris, Saint-Mande 94160, France.

Paul Chiron (P)

Hôpital d'Instruction des Armées BEGIN, Service d'urologie, 69 avenue de Paris, Saint-Mande 94160, France.

Mathilde Sollier (M)

Hôpital d'Instruction des Armées BEGIN, Service d'endocrinologie, 69 avenue de Paris, Saint-Mande 94160, France.

Sika Nassouri (S)

Hôpital d'Instruction des Armées BEGIN, Service d'endocrinologie, 69 avenue de Paris, Saint-Mande 94160, France.

Lionel Groussin (L)

Hôpital COCHIN, Service d'endocrinologie, 27 rue du Faubourg Saint Jacques, Paris 75014, France.

Mathilde Sibony (M)

Hôpital COCHIN, Service d'anatomopathologie, 27 rue du Faubourg Saint Jacques, Paris 75014, France.

Claire Goursaud (C)

Hospices Civils de Lyon-Bron, Laboratoire de Biochimie et Biologie Moléculaire Grand Est, Lyon 69000, France.

Florence Roucher-Boulez (F)

Hospices Civils de Lyon-Bron, Laboratoire de Biochimie et Biologie Moléculaire Grand Est, Lyon 69000, France.

Lyse Bordier (L)

Hôpital d'Instruction des Armées BEGIN, Service d'endocrinologie, 69 avenue de Paris, Saint-Mande 94160, France.

Classifications MeSH