Clinical characterization of a novel alpha1-antitrypsin null variant: PiQ0

Alpha1-antitrypsin Alpha1-antitrypsin deficiency Chronic obstructive pulmonary disease PiQ0Heidelberg SERPINA1

Journal

Respiratory medicine case reports
ISSN: 2213-0071
Titre abrégé: Respir Med Case Rep
Pays: England
ID NLM: 101604463

Informations de publication

Date de publication:
2022
Historique:
received: 03 11 2021
revised: 02 12 2021
accepted: 30 12 2021
entrez: 14 1 2022
pubmed: 15 1 2022
medline: 15 1 2022
Statut: epublish

Résumé

The clinical characterization of a null variant of

Identifiants

pubmed: 35028284
doi: 10.1016/j.rmcr.2021.101570
pii: S2213-0071(21)00232-X
pmc: PMC8741486
doi:

Types de publication

Case Reports

Langues

eng

Pagination

101570

Informations de copyright

© 2022 The Authors. Published by Elsevier Ltd.

Déclaration de conflit d'intérêts

Maria A. Presotto, Martina Veith, Kai Schlamp, Markus Polke and Felix F.J. Herth have no conflicts of interest. Franziska Trudzinski reported personal fees from GlaxoSmithKline, Novartis and CSL Behring, outside the submitted work. Ralf Eberhardt received personal fees from Pfizer, Pulmonx, Olympus and Broncus outside the submitted work. Frederik Trinkmann received travel support from Actelion, Berlin Chemie, Boehringer Ingelheim, Chiesi, Novartis, Mundipharma, and TEVA, as well as speaker or consultation fees from AstraZeneca, Berlin Chemie, Boehringer Ingelheim, Bristol-Myers Squibb, Chiesi, GlaxoSmithKline, Novartis, Roche, and Sanofi-Aventis, all outside the submitted work.

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Auteurs

Maria A Presotto (MA)

Department of Pneumology and Critical Care Medicine, Thoraxklinik University of Heidelberg, Translational Lung Research Center Heidelberg (TLRC-H), German Center for Lung Research (DZL), Heidelberg, Germany.

Martina Veith (M)

University Medical Centre Giessen and Marburg, Philipps-University, Dept of Medicine, Pulmonary and Critical Care Medicine, Member of the German Centre for Lung Research (DZL), Marburg, Germany.

Frederik Trinkmann (F)

Department of Pneumology and Critical Care Medicine, Thoraxklinik University of Heidelberg, Translational Lung Research Center Heidelberg (TLRC-H), German Center for Lung Research (DZL), Heidelberg, Germany.

Kai Schlamp (K)

Department of Radiology, Thoraxklinik University of Heidelberg, Translational Lung Research Center Heidelberg (TLRC-H), German Center for Lung Research (DZL), Heidelberg, Germany.

Markus Polke (M)

Department of Pneumology and Critical Care Medicine, Thoraxklinik University of Heidelberg, Translational Lung Research Center Heidelberg (TLRC-H), German Center for Lung Research (DZL), Heidelberg, Germany.

Ralf Eberhardt (R)

Department of Pneumology and Critical Care Medicine, Asklepios Klinik Barmbek, Hamburg, Germany.

Felix Herth (F)

Department of Pneumology and Critical Care Medicine, Thoraxklinik University of Heidelberg, Translational Lung Research Center Heidelberg (TLRC-H), German Center for Lung Research (DZL), Heidelberg, Germany.

Franziska C Trudzinski (FC)

Department of Pneumology and Critical Care Medicine, Thoraxklinik University of Heidelberg, Translational Lung Research Center Heidelberg (TLRC-H), German Center for Lung Research (DZL), Heidelberg, Germany.

Classifications MeSH