Pediatric Restrictive Cardiomyopathies.

cardiomyopathy heart transplant (HTx) pediatric cardiomyopathies restrictive cardiomyopathy (RCM) sarcomeric cardiomyopathy

Journal

Frontiers in pediatrics
ISSN: 2296-2360
Titre abrégé: Front Pediatr
Pays: Switzerland
ID NLM: 101615492

Informations de publication

Date de publication:
2021
Historique:
received: 21 07 2021
accepted: 28 12 2021
entrez: 11 2 2022
pubmed: 12 2 2022
medline: 12 2 2022
Statut: epublish

Résumé

Restrictive cardiomyopathy (RCM) is the least frequent phenotype among pediatric heart muscle diseases, representing only 2.5-3% of all cardiomyopathies diagnosed during childhood. Pediatric RCM has a poor prognosis, high incidence of pulmonary hypertension (PH), thromboembolic events, and sudden death, is less amenable to medical or surgical treatment with high mortality rates. In this

Identifiants

pubmed: 35145940
doi: 10.3389/fped.2021.745365
pmc: PMC8822222
doi:

Types de publication

Journal Article Review

Langues

eng

Pagination

745365

Informations de copyright

Copyright © 2022 Ditaranto, Caponetti, Ferrara, Parisi, Minnucci, Chiti, Baldassarre, Di Nicola, Bonetti, Hasan, Potena, Galiè, Ragni and Biagini.

Déclaration de conflit d'intérêts

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

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Auteurs

Raffaello Ditaranto (R)

Cardiology Unit, Department of Experimental, Diagnostic and Specialty Medicine, IRCCS, Sant'Orsola Hospital, University of Bologna, Bologna, Italy.

Angelo Giuseppe Caponetti (AG)

Cardiology Unit, Department of Experimental, Diagnostic and Specialty Medicine, IRCCS, Sant'Orsola Hospital, University of Bologna, Bologna, Italy.

Valentina Ferrara (V)

Cardiology Unit, Department of Experimental, Diagnostic and Specialty Medicine, IRCCS, Sant'Orsola Hospital, University of Bologna, Bologna, Italy.

Vanda Parisi (V)

Cardiology Unit, Department of Experimental, Diagnostic and Specialty Medicine, IRCCS, Sant'Orsola Hospital, University of Bologna, Bologna, Italy.

Matteo Minnucci (M)

Cardiology Unit, Department of Experimental, Diagnostic and Specialty Medicine, IRCCS, Sant'Orsola Hospital, University of Bologna, Bologna, Italy.

Chiara Chiti (C)

Cardiology Unit, Department of Experimental, Diagnostic and Specialty Medicine, IRCCS, Sant'Orsola Hospital, University of Bologna, Bologna, Italy.

Riccardo Baldassarre (R)

Cardiology Unit, Department of Experimental, Diagnostic and Specialty Medicine, IRCCS, Sant'Orsola Hospital, University of Bologna, Bologna, Italy.

Federico Di Nicola (F)

Cardiology Unit, Department of Experimental, Diagnostic and Specialty Medicine, IRCCS, Sant'Orsola Hospital, University of Bologna, Bologna, Italy.

Simone Bonetti (S)

Pediatric Cardiac Surgery and GUCH Unit, IRCCS, Sant'Orsola Hospital, University of Bologna, Bologna, Italy.

Tammam Hasan (T)

Pediatric Cardiac Surgery and GUCH Unit, IRCCS, Sant'Orsola Hospital, University of Bologna, Bologna, Italy.

Luciano Potena (L)

Cardiology Unit, Department of Experimental, Diagnostic and Specialty Medicine, IRCCS, Sant'Orsola Hospital, University of Bologna, Bologna, Italy.

Nazzareno Galiè (N)

Cardiology Unit, Department of Experimental, Diagnostic and Specialty Medicine, IRCCS, Sant'Orsola Hospital, University of Bologna, Bologna, Italy.

Luca Ragni (L)

Pediatric Cardiac Surgery and GUCH Unit, IRCCS, Sant'Orsola Hospital, University of Bologna, Bologna, Italy.

Elena Biagini (E)

Cardiology Unit, Department of Experimental, Diagnostic and Specialty Medicine, IRCCS, Sant'Orsola Hospital, University of Bologna, Bologna, Italy.

Classifications MeSH