Coexistence of Renin-independent Aldosterone Secretion and Multiple Endocrine Neoplasia Type 1 Within a Family.

independent aldosterone secretion multiple endocrine neoplasia type 1 renin

Journal

Journal of the Endocrine Society
ISSN: 2472-1972
Titre abrégé: J Endocr Soc
Pays: United States
ID NLM: 101697997

Informations de publication

Date de publication:
01 Mar 2022
Historique:
received: 09 07 2021
entrez: 21 2 2022
pubmed: 22 2 2022
medline: 22 2 2022
Statut: epublish

Résumé

Primary aldosteronism (PA) is a state of renin-independent aldosterone secretion that can range from subclinical to overt. Some normotensive individuals for whom PA screening is not routinely recommended are reported to fulfill the loading test criterion used for the diagnosis of PA. Multiple endocrine neoplasia type 1 (MEN1) is an autosomal dominant disorder characterized by the development of various endocrine tumors. Cases of PA associated with MEN1 have been reported; however, there has been no previous report on renin-independent aldosterone secretion within a family with MEN1. Herein, we present the case of a normotensive family presenting with both MEN1 and renin-independent aldosterone secretion. A 49-year-old man was admitted to our hospital for PA evaluation owing to the plasma aldosterone concentration/plasma renin activity ratio being greater than the screening cut-off value; the patient was normotensive. The patient had a history of left nephrectomy and adrenalectomy for left renal carcinoma and adrenal tumor at the age of 39 years. Subsequently, he was diagnosed with MEN1 concurrent with primary hyperparathyroidism, insulinoma, and novel

Identifiants

pubmed: 35187382
doi: 10.1210/jendso/bvac009
pii: bvac009
pmc: PMC8852679
doi:

Types de publication

Case Reports

Langues

eng

Pagination

bvac009

Informations de copyright

© The Author(s) 2022. Published by Oxford University Press on behalf of the Endocrine Society.

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Auteurs

Yoshinari Obata (Y)

Department of Diabetes and Endocrinology, Osaka Police Hospital, Osaka, Japan.

Kana Takayama (K)

Department of Diabetes and Endocrinology, Osaka Police Hospital, Osaka, Japan.

Yumiko Maruo (Y)

Department of Diabetes and Endocrinology, Osaka Police Hospital, Osaka, Japan.

Hiroki Yamaguchi (H)

Department of Diabetes and Endocrinology, Osaka Police Hospital, Osaka, Japan.

Kohei Fujii (K)

Department of Metabolic Medicine, Graduate School of Medicine, Osaka University, Osaka, Japan.

Sonyun Hata (S)

Diabetes Center, National Hospital Organization Osaka Medical Center, Osaka, Japan.

Yuri Togawa (Y)

Department of Internal Medicine, Japan Community Healthcare Organization, Osaka Hospital, Osaka, Japan.

Azusa Sanda (A)

Department of Internal Medicine, Japan Community Healthcare Organization, Osaka Hospital, Osaka, Japan.

Motohiro Kosugi (M)

Department of Diabetes and Endocrinology, Osaka Police Hospital, Osaka, Japan.

Yoji Hazama (Y)

Department of Diabetes and Endocrinology, Osaka Police Hospital, Osaka, Japan.

Tetsuyuki Yasuda (T)

Department of Diabetes and Endocrinology, Osaka Police Hospital, Osaka, Japan.

Classifications MeSH