Biliary Atresia in 2021: Epidemiology, Screening and Public Policy.
biliary atresia
epidemiology
newborn screening
pediatric liver disease
public health
Journal
Journal of clinical medicine
ISSN: 2077-0383
Titre abrégé: J Clin Med
Pays: Switzerland
ID NLM: 101606588
Informations de publication
Date de publication:
14 Feb 2022
14 Feb 2022
Historique:
received:
24
12
2021
revised:
05
02
2022
accepted:
09
02
2022
entrez:
25
2
2022
pubmed:
26
2
2022
medline:
26
2
2022
Statut:
epublish
Résumé
Biliary atresia (BA) is a rare newborn liver disease with significant morbidity and mortality, especially if not recognized and treated early in life. It is the most common cause of liver-related death in children and the leading indication for liver transplantation in the pediatric population. Timely intervention with a Kasai portoenterostomy (KPE) can significantly improve prognosis. Delayed disease recognition, late patient referral, and untimely surgery remains a worldwide problem. This article will focus on biliary atresia from a global public health perspective, including disease epidemiology, current national screening programs, and their impact on outcome, as well as new and novel BA screening initiatives. Policy challenges for the implementation of BA screening programs will also be discussed, highlighting examples from the North American, European, and Asian experience.
Identifiants
pubmed: 35207269
pii: jcm11040999
doi: 10.3390/jcm11040999
pmc: PMC8876662
pii:
doi:
Types de publication
Journal Article
Langues
eng
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