The role of adrenal venous sampling (AVS) in primary bilateral macronodular adrenocortical hyperplasia (PBMAH): a study of 16 patients.


Journal

Endocrine
ISSN: 1559-0100
Titre abrégé: Endocrine
Pays: United States
ID NLM: 9434444

Informations de publication

Date de publication:
05 2022
Historique:
received: 05 11 2021
accepted: 16 02 2022
pubmed: 12 3 2022
medline: 7 5 2022
entrez: 11 3 2022
Statut: ppublish

Résumé

Primary bilateral macronodular adrenocortical hyperplasia (PBMAH) is a rare cause of ACTH-independent Cushing's syndrome. Current guidelines recommend bilateral adrenalectomy for PBMAH, but several studies showed clinical effectiveness of unilateral adrenalectomy despite bilateral disease in selected patients. Our aim was to evaluate the gain of information which can be obtained through adrenal venous sampling (AVS) based cortisol lateralization ratios for guidance of unilateral adrenalectomy. We performed a retrospective analysis of 16 patients with PBMAH and clinical overt cortisol secretion in three centers METHODS: Selectivity of adrenal vein sampling during AVS was defined as a gradient of cortisol or a reference adrenal hormone ≥2.0 between adrenal and peripheral vein. Lateralization was assumed if the dominant to non-dominant ratio of cortisol to reference hormone was ≥4.0. AVS was technically successful in all patients based on absolute cortisol levels and in 13 of 16 patients (81%) based on reference hormone levels. Lateralization was documented in 8 of 16 patients. In patients with lateralization, in 5 of 8 cases this occurred toward morphologically larger adrenals, while in 3 patients lateralization was present in bilaterally identical adrenals. The combined volume of adrenals correlated positively with urinary free cortisol, suggesting that adrenal size is the dominant determinant of cortisol secretion. In this study the gain of information through AVS for unilateral adrenalectomy was limited in patients with PBMAH and marked adrenal asymmetry.

Identifiants

pubmed: 35274284
doi: 10.1007/s12020-022-03020-z
pii: 10.1007/s12020-022-03020-z
pmc: PMC9068666
doi:

Substances chimiques

Hydrocortisone WI4X0X7BPJ

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

434-445

Informations de copyright

© 2022. The Author(s).

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Auteurs

German Rubinstein (G)

Medizinische Klinik und Poliklinik IV, Klinikum der Universität München, München, Germany.

Andrea Osswald (A)

Medizinische Klinik und Poliklinik IV, Klinikum der Universität München, München, Germany.

Leah Theresa Braun (LT)

Medizinische Klinik und Poliklinik IV, Klinikum der Universität München, München, Germany.

Frederick Vogel (F)

Medizinische Klinik und Poliklinik IV, Klinikum der Universität München, München, Germany.

Matthias Kroiss (M)

Medizinische Klinik und Poliklinik IV, Klinikum der Universität München, München, Germany.
Department of Internal Medicine I, Division of Endocrinology and Diabetes, University of Würzburg, University Hospital Würzburg, Würzburg, Germany.

Stefan Pilz (S)

Division of Endocrinology and Diabetology, Department of Internal Medicine, Medical University of Graz, Graz, Austria.

Sinan Deniz (S)

Klinik und Poliklinik für Radiologie, Klinikum der Universität München, München, Germany.

Laura Aigner (L)

Klinik und Poliklinik für Radiologie, Klinikum der Universität München, München, Germany.
Department for Diagnostic and Interventional Radiology and Neuroradiology, Klinikverbund Allgäu, Kempten, Germany.

Thomas Knösel (T)

Pathologisches Institut, Klinikum der Universität München, München, Deutschland.

Jérôme Bertherat (J)

Université de Paris, 75006, Paris, France.
Department of Endocrinology, Center for Rare Adrenal Diseases, Assistance Publique-Hôpitaux de Paris, Hôpital Cochin, 75014, Paris, France.

Lucas Bouys (L)

Université de Paris, 75006, Paris, France.
Department of Endocrinology, Center for Rare Adrenal Diseases, Assistance Publique-Hôpitaux de Paris, Hôpital Cochin, 75014, Paris, France.

Roland Ladurner (R)

Klinik für Allgemeine, Unfall- und Wiederherstellungschirurgie, Campus Innenstadt, Klinikum der Universität München, München, Germany.

Anna Riester (A)

Medizinische Klinik und Poliklinik IV, Klinikum der Universität München, München, Germany.

Martin Bidlingmaier (M)

Medizinische Klinik und Poliklinik IV, Klinikum der Universität München, München, Germany.

Felix Beuschlein (F)

Medizinische Klinik und Poliklinik IV, Klinikum der Universität München, München, Germany.
Klinik für Endokrinologie, Diabetologie und Klinische Ernährung, Universitätsspital Zürich (USZ) and Universität Zürich (UZH), Zürich, Switzerland.

Martin Reincke (M)

Medizinische Klinik und Poliklinik IV, Klinikum der Universität München, München, Germany. martin.reincke@med.uni-muenchen.de.

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