Posterior Fossa Tumours in the First Year of Life: A Two-Centre Retrospective Study.

Atypical Teratoid/Rhabdoid Tumour astrocytoma ependymoma infants infratentorial tumours medulloblastoma posterior fossa tumours

Journal

Diagnostics (Basel, Switzerland)
ISSN: 2075-4418
Titre abrégé: Diagnostics (Basel)
Pays: Switzerland
ID NLM: 101658402

Informations de publication

Date de publication:
04 Mar 2022
Historique:
received: 07 02 2022
revised: 25 02 2022
accepted: 01 03 2022
entrez: 25 3 2022
pubmed: 26 3 2022
medline: 26 3 2022
Statut: epublish

Résumé

Posterior fossa tumours (PFTs) in infants are very rare, and information on these tumours is scarce in the literature. This retrospective study reports their pathological characteristics and describes surgical aspects and treatment outcomes. A two-centre cohort of infants with PFTs treated from 2007 to 2018 was retrospectively reviewed. Patient characteristics, clinical, and treatment data were reviewed. Survival curves for progression-free survival (PFS) and overall survival (OS) were generated. Thirty-three infants were retrieved. There were 11 low grade and 22 high-grade tumours. The most common presenting symptom was intracranial hypertension. Fifteen children out of thirty-three progressed. Five-year PFS was significantly lower in children with high-grade tumours (38.3%) than those with low-grade tumours (69.3%),

Identifiants

pubmed: 35328188
pii: diagnostics12030635
doi: 10.3390/diagnostics12030635
pmc: PMC8947426
pii:
doi:

Types de publication

Journal Article

Langues

eng

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Auteurs

Stefania Picariello (S)

Neuro-Oncology Unit, Department of Paediatric Oncology, Santobono-Pausilipon Children's Hospital, Via Mario Fiore 6, 80129 Naples, Italy.
Department of Women, Child and General and Specialized Surgery, University of Campania "Luigi Vanvitelli", Via Luigi De Crecchio 4, 80138 Naples, Italy.

Pietro Spennato (P)

Division of Neurosurgery, Department of Neurosciences, Santobono-Pausilipon Children's Hospital, Via Mario Fiore 6, 80129 Naples, Italy.

Jonathan Roth (J)

Departments of Pediatric Neurosurgery, Dana Children's Hospital, Tel Aviv Medical Center, Tel Aviv University, 6 Weizmann St., Tel Aviv 6423906, Israel.

Nir Shimony (N)

Departments of Pediatric Neurosurgery, Dana Children's Hospital, Tel Aviv Medical Center, Tel Aviv University, 6 Weizmann St., Tel Aviv 6423906, Israel.

Alessandra Marini (A)

Department of Neurosurgery, Ospedale Santa Maria della Misericordia di Perugia, Piazzale Giorgio Menghini 3, 06129 Perugia, Italy.

Lucia De Martino (L)

Neuro-Oncology Unit, Department of Paediatric Oncology, Santobono-Pausilipon Children's Hospital, Via Mario Fiore 6, 80129 Naples, Italy.

Giancarlo Nicosia (G)

Neurosurgery Unit, San Pio Hospital, Via Pacevecchia 53, 82100 Benevento, Italy.

Giuseppe Mirone (G)

Division of Neurosurgery, Department of Neurosciences, Santobono-Pausilipon Children's Hospital, Via Mario Fiore 6, 80129 Naples, Italy.

Maria Serena De Santi (MS)

Division of Neurosurgery, Department of Neurosciences, Santobono-Pausilipon Children's Hospital, Via Mario Fiore 6, 80129 Naples, Italy.

Fabio Savoia (F)

Childhood Cancer Registry of Campania, Santobono-Pausilipon Children's Hospital, Via della Croce Rossa 8, 80129 Naples, Italy.

Maria Elena Errico (ME)

Department of Pathology, Santobono-Pausilipon Children's Hospital, Via Posillipo 226, 80123 Naples, Italy.

Lucia Quaglietta (L)

Neuro-Oncology Unit, Department of Paediatric Oncology, Santobono-Pausilipon Children's Hospital, Via Mario Fiore 6, 80129 Naples, Italy.

Shlomi Costantini (S)

Departments of Pediatric Neurosurgery, Dana Children's Hospital, Tel Aviv Medical Center, Tel Aviv University, 6 Weizmann St., Tel Aviv 6423906, Israel.

Giuseppe Cinalli (G)

Division of Neurosurgery, Department of Neurosciences, Santobono-Pausilipon Children's Hospital, Via Mario Fiore 6, 80129 Naples, Italy.

Classifications MeSH