Diencephalic Syndrome Due to Optic Pathway Gliomas in Pediatric Patients: An Italian Multicenter Study.

NF1 chemotherapy diencephalic syndrome long-term outcomes optic pathway glioma pediatric

Journal

Diagnostics (Basel, Switzerland)
ISSN: 2075-4418
Titre abrégé: Diagnostics (Basel)
Pays: Switzerland
ID NLM: 101658402

Informations de publication

Date de publication:
09 Mar 2022
Historique:
received: 31 01 2022
revised: 19 02 2022
accepted: 02 03 2022
entrez: 25 3 2022
pubmed: 26 3 2022
medline: 26 3 2022
Statut: epublish

Résumé

Diencephalic syndrome (DS) is a rare pediatric condition associated with optic pathway gliomas (OPGs). Since they are slow-growing tumors, their diagnosis might be delayed, with consequences on long-term outcomes. We present a multicenter case series of nine children with DS associated with OPG, with the aim of providing relevant details about mortality and long-term sequelae. We retrospectively identified nine children (6 M) with DS (median age 14 months, range 3-26 months). Four patients had NF1-related OPGs. Children with NF1 were significantly older than sporadic cases (median (range) age in months: 21.2 (14-26) versus 10 (3-17);

Identifiants

pubmed: 35328218
pii: diagnostics12030664
doi: 10.3390/diagnostics12030664
pmc: PMC8947184
pii:
doi:

Types de publication

Journal Article

Langues

eng

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Auteurs

Lucia De Martino (L)

Neurooncology Unit, Department of Pediatric Oncology, Santobono-Pausilipon Children's Hospital, via M. Fiore n° 6, 80129 Naples, Italy.

Stefania Picariello (S)

Neurooncology Unit, Department of Pediatric Oncology, Santobono-Pausilipon Children's Hospital, via M. Fiore n° 6, 80129 Naples, Italy.
Department of Woman, Child and General and Specialized Surgery, University of Campania "Luigi Vanvitelli", via L. De Crecchio n° 2, 80138 Naples, Italy.

Silvia Triarico (S)

Pediatric Oncology Unit, Fondazione Policlinico Universitario A. Gemelli IRCCS, Largo A. Gemelli, 00168 Rome, Italy.

Nicola Improda (N)

Emergency Unit, Department of Emergency, Santobono-Pausilipon Children's Hospital, via M. Fiore n° 6, 80129 Naples, Italy.
Section of Pediatrics, Department of Translational and Medical Sciences, University Federico II, via S. Pansini n° 5, 80138 Naples, Italy.

Pietro Spennato (P)

Pediatric Neurosurgery Unit, Department of Pediatric Neurosciences, Santobono-Pausilipon Children's Hospital, via M. Fiore n° 6, 80129 Naples, Italy.

Michele Antonio Capozza (MA)

Pediatric Oncology Unit, Department of Pediatric Oncology, Santobono-Pausilipon Children's Hospital, via Posillipo n° 226, 80123 Naples, Italy.

Anna Grandone (A)

Department of Woman, Child and General and Specialized Surgery, University of Campania "Luigi Vanvitelli", via L. De Crecchio n° 2, 80138 Naples, Italy.

Claudia Santoro (C)

Department of Woman, Child and General and Specialized Surgery, University of Campania "Luigi Vanvitelli", via L. De Crecchio n° 2, 80138 Naples, Italy.
Clinic of Child and Adolescent Neuropsychiatry, Department of Mental and Physical Health, and Preventive Medicine, Università degli Studi della Campania "Luigi Vanvitelli", via L. De Crecchio n° 2, 80138 Naples, Italy.

Daniela Cioffi (D)

Pediatric Endocrinology Unit, Department of Pediatrics, Santobono-Pausilipon Children's Hospital, via M. Fiore n° 6, 80129 Naples, Italy.

Giorgio Attinà (G)

Pediatric Oncology Unit, Fondazione Policlinico Universitario A. Gemelli IRCCS, Largo A. Gemelli, 00168 Rome, Italy.

Giuseppe Cinalli (G)

Pediatric Neurosurgery Unit, Department of Pediatric Neurosciences, Santobono-Pausilipon Children's Hospital, via M. Fiore n° 6, 80129 Naples, Italy.

Antonio Ruggiero (A)

Pediatric Oncology Unit, Fondazione Policlinico Universitario A. Gemelli IRCCS, Largo A. Gemelli, 00168 Rome, Italy.

Lucia Quaglietta (L)

Neurooncology Unit, Department of Pediatric Oncology, Santobono-Pausilipon Children's Hospital, via M. Fiore n° 6, 80129 Naples, Italy.

Classifications MeSH