Prenatal Diagnosis and Outcome of Scimitar Syndrome: A Case Series of Six Patients.
congenital heart defect
fetal echocardiography
partial anomalous pulmonary vein connection
prenatal ultrasound
scimitar syndrome
Journal
Journal of clinical medicine
ISSN: 2077-0383
Titre abrégé: J Clin Med
Pays: Switzerland
ID NLM: 101606588
Informations de publication
Date de publication:
18 Mar 2022
18 Mar 2022
Historique:
received:
11
02
2022
revised:
12
03
2022
accepted:
16
03
2022
entrez:
25
3
2022
pubmed:
26
3
2022
medline:
26
3
2022
Statut:
epublish
Résumé
Scimitar syndrome is a rare disease characterized by hypoplasia of the right lung and partial anomalous pulmonary venous drainage to the inferior vena cava. All cases with a prenatal diagnosis of scimitar syndrome with or without associated malformations in an 18-year period (2000-2018) in two large tertiary referral centers (University of Bonn and University of Cologne, Germany) were retrospectively reviewed for the intrauterine course and postnatal outcome. Six cases were diagnosed in the study period. All presented with hypoplasia of the right lung, right-sided mediastinal shift, and abnormal pulmonary venous drainage to the inferior vena cava. Systemic arterial blood supply to the right lung, albeit postnatally present in all cases, could not be detected prenatally. Major associated anomalies were present in all cases and included atrial septal defect (
Identifiants
pubmed: 35330021
pii: jcm11061696
doi: 10.3390/jcm11061696
pmc: PMC8954158
pii:
doi:
Types de publication
Journal Article
Langues
eng
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