Pulmonary 99mTc-HMDP uptake correlates with restrictive ventilatory defects and abnormal lung reactance in transthyretin cardiac amyloidosis patients.
99mTc-HMDP
Aerobic capacity
Cardiac amyloidosis
Lung function tests
Transthyretin
Journal
Respiratory research
ISSN: 1465-993X
Titre abrégé: Respir Res
Pays: England
ID NLM: 101090633
Informations de publication
Date de publication:
27 Mar 2022
27 Mar 2022
Historique:
received:
28
10
2021
accepted:
15
03
2022
entrez:
29
3
2022
pubmed:
30
3
2022
medline:
5
4
2022
Statut:
epublish
Résumé
Pulmonary involvement in individuals with transthyretin cardiac amyloidosis is unclear. The aim of this study was to quantify We prospectively enrolled 20 patients with biopsy-proven ATTRv cardiac amyloidosis and 20 control subjects. Cardiac involvement was confirmed by echocardiography and nuclear imaging using Pulmonary tracer uptake estimated by lung to rib retention ratio was higher in ATTRv amyloidosis patients compared with control subjects: median 0.62 (0.55-0.69) vs 0.51 (0.46-0.60); p = 0.014. Analysis of relation between lung Our study suggests that some grade of pulmonary retention of
Sections du résumé
BACKGROUND
BACKGROUND
Pulmonary involvement in individuals with transthyretin cardiac amyloidosis is unclear. The aim of this study was to quantify
METHODS
METHODS
We prospectively enrolled 20 patients with biopsy-proven ATTRv cardiac amyloidosis and 20 control subjects. Cardiac involvement was confirmed by echocardiography and nuclear imaging using
RESULTS
RESULTS
Pulmonary tracer uptake estimated by lung to rib retention ratio was higher in ATTRv amyloidosis patients compared with control subjects: median 0.62 (0.55-0.69) vs 0.51 (0.46-0.60); p = 0.014. Analysis of relation between lung
CONCLUSION
CONCLUSIONS
Our study suggests that some grade of pulmonary retention of
Identifiants
pubmed: 35346209
doi: 10.1186/s12931-022-01995-x
pii: 10.1186/s12931-022-01995-x
pmc: PMC8962108
doi:
Substances chimiques
Prealbumin
0
Radiopharmaceuticals
0
Technetium Tc 99m Medronate
X89XV46R07
Types de publication
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
72Informations de copyright
© 2022. The Author(s).
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