Deciphering Genetic Alterations of Hairy Cell Leukemia and Hairy Cell Leukemia-like Disorders in 98 Patients.

BRAF HCL KLF2 MAP2K1 genetic alterations hairy cell leukemia hairy cell leukemia variant (vHCL) hairy cell leukemia-like disorders splenic diffuse red pulp lymphoma (SDRPL)

Journal

Cancers
ISSN: 2072-6694
Titre abrégé: Cancers (Basel)
Pays: Switzerland
ID NLM: 101526829

Informations de publication

Date de publication:
10 Apr 2022
Historique:
received: 28 02 2022
revised: 05 04 2022
accepted: 06 04 2022
entrez: 23 4 2022
pubmed: 24 4 2022
medline: 24 4 2022
Statut: epublish

Résumé

Hairy cell leukemia (cHCL) patients have, in most cases, a specific clinical and biological presentation with splenomegaly, anemia, leukopenia, neutropenia, monocytopenia and/or thrombocytopenia, identification of hairy cells that express CD103, CD123, CD25, CD11c and identification of the V600E mutation in the B-Raf proto-oncogene (

Identifiants

pubmed: 35454811
pii: cancers14081904
doi: 10.3390/cancers14081904
pmc: PMC9028144
pii:
doi:

Types de publication

Journal Article

Langues

eng

Subventions

Organisme : CHU CAEN
ID : ARPI2017

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Auteurs

Elsa Maitre (E)

INSERM U1245, Normandie University, UNIROUEN, UNICAEN, 14032 Caen, France.
Laboratory of Hematology, University Hospital Caen, Avenue de la Côte de Nacre, CEDEX, 14033 Caen, France.
Structure Fédérative SF-MOCAE, University Hospital Caen, Avenue de la Côte de Nacre, CEDEX, 14033 Caen, France.

Cécile Tomowiak (C)

Department of Hematology, University Hospital Poitiers, 2 rue Milétrie, 86000 Poitiers, France.

Benjamin Lebecque (B)

Laboratory Hematology, University Hospital Clermont-Ferrand, 58 rue Montalembert, 63000 Clermont-Ferrrand, France.

Fontanet Bijou (F)

Department of Hematology, Institut Bergonié, 229 Cours de l'Argonne, CEDEX, 33079 Bordeaux, France.

Khaled Benabed (K)

Department of Hematology, Centre Hospitalier Public du Cotentin, 46 rue du Val de Saire, 50100 Cherbourg-en-Cotentin, France.
Department of Hematology, Centre Henri Becquerel, 1 rue d'Amiens, CEDEX, 76038 Rouen, France.

Dina Naguib (D)

Laboratory of Hematology, University Hospital Caen, Avenue de la Côte de Nacre, CEDEX, 14033 Caen, France.
Structure Fédérative SF-MOCAE, University Hospital Caen, Avenue de la Côte de Nacre, CEDEX, 14033 Caen, France.

Pauline Kerneves (P)

Laboratory of Hematology, University Hospital Caen, Avenue de la Côte de Nacre, CEDEX, 14033 Caen, France.
Structure Fédérative SF-MOCAE, University Hospital Caen, Avenue de la Côte de Nacre, CEDEX, 14033 Caen, France.

Edouard Cornet (E)

INSERM U1245, Normandie University, UNIROUEN, UNICAEN, 14032 Caen, France.
Laboratory of Hematology, University Hospital Caen, Avenue de la Côte de Nacre, CEDEX, 14033 Caen, France.

Pierre-Julien Viailly (PJ)

INSERM U1245, Normandie University, UNIROUEN, UNICAEN, 14032 Caen, France.
Department of Hematology, Centre Henri Becquerel, 1 rue d'Amiens, CEDEX, 76038 Rouen, France.
Hematology Institute, University Hospital Caen, Avenue de la Côte de Nacre, 14033 Caen, France.

Jeffrey Arsham (J)

Department of Hematology, University Hospital Poitiers, 2 rue Milétrie, 86000 Poitiers, France.

Brigitte Sola (B)

INSERM U1245, Normandie University, UNIROUEN, UNICAEN, 14032 Caen, France.

Fabrice Jardin (F)

INSERM U1245, Normandie University, UNIROUEN, UNICAEN, 14032 Caen, France.
Department of Hematology, Centre Henri Becquerel, 1 rue d'Amiens, CEDEX, 76038 Rouen, France.

Xavier Troussard (X)

INSERM U1245, Normandie University, UNIROUEN, UNICAEN, 14032 Caen, France.
Laboratory of Hematology, University Hospital Caen, Avenue de la Côte de Nacre, CEDEX, 14033 Caen, France.
Hematology Institute, University Hospital Caen, Avenue de la Côte de Nacre, 14033 Caen, France.

Classifications MeSH