Facial diplegia with paresthesia associated with anti-GD1a antibodies.

Anti-ganglioside antibodies Guillain-Barré syndrome demyelinating disease facial diplegia peripheral neuropathy polyneuropathy

Journal

Proceedings (Baylor University. Medical Center)
ISSN: 0899-8280
Titre abrégé: Proc (Bayl Univ Med Cent)
Pays: United States
ID NLM: 9302033

Informations de publication

Date de publication:
2022
Historique:
entrez: 6 5 2022
pubmed: 7 5 2022
medline: 7 5 2022
Statut: epublish

Résumé

A 26-year-old previously healthy man presented with progressive facial diplegia and sensory deficits to pinprick in a stocking-glove distribution. Lumbar puncture revealed cytoalbuminologic dissociation, and a nerve conduction study of the right facial nerve demonstrated a proximal demyelinating process. He was started on intravenous immunoglobulin given concern for a Guillain-Barré syndrome variant, and his symptoms improved over several days. This case illustrates the clinical features of facial diplegia with paresthesias, a rare variant of Guillain-Barré syndrome. Unlike most reported cases of facial diplegia with paresthesias that have demonstrated positive anti-ganglioside M2 antibodies, this case is unique given the positivity of anti-ganglioside D1a IgG/IgM antibodies.

Identifiants

pubmed: 35518821
doi: 10.1080/08998280.2022.2043679
pii: 2043679
pmc: PMC9037508
doi:

Types de publication

Case Reports

Langues

eng

Pagination

387-388

Informations de copyright

Copyright © 2022 Baylor University Medical Center.

Références

Ann Neurol. 1999 Feb;45(2):168-73
pubmed: 9989618
N Engl J Med. 2012 Jun 14;366(24):2294-304
pubmed: 22694000
J Neurol. 2009 Nov;256(11):1899-905
pubmed: 19633904
J Peripher Nerv Syst. 2015 Mar;20(1):32-6
pubmed: 25975218
Intern Med. 2015;54(3):345-7
pubmed: 25748745

Auteurs

Jason Strawbridge (J)

David Geffen School of Medicine, University of California, Los Angeles, Los Angeles, California.

Katherine A Fu (KA)

Department of Neurology, University of California, Los Angeles, Los Angeles, California.

Joy Chan (J)

Sacramento VA Medical Center, Sacramento, California.

William Flavin (W)

Department of Neurology, University of California, Los Angeles, Los Angeles, California.

Joss Cohen (J)

Department of Neurology, University of California, Los Angeles, Los Angeles, California.

Inna Keselman (I)

Department of Neurology, University of California, Los Angeles, Los Angeles, California.

Perry Shieh (P)

Department of Neurology, University of California, Los Angeles, Los Angeles, California.

Classifications MeSH