Recurrent Germline Variant in


Journal

International journal of molecular sciences
ISSN: 1422-0067
Titre abrégé: Int J Mol Sci
Pays: Switzerland
ID NLM: 101092791

Informations de publication

Date de publication:
05 May 2022
Historique:
received: 12 04 2022
accepted: 02 05 2022
entrez: 14 5 2022
pubmed: 15 5 2022
medline: 18 5 2022
Statut: epublish

Résumé

Somatic loss of function mutations in cohesin genes are frequently associated with various cancer types, while cohesin disruption in the germline causes cohesinopathies such as Cornelia-de-Lange syndrome (CdLS). Here, we present the discovery of a recurrent heterozygous

Identifiants

pubmed: 35563565
pii: ijms23095174
doi: 10.3390/ijms23095174
pmc: PMC9106003
pii:
doi:

Substances chimiques

Cell Cycle Proteins 0
DNA-Binding Proteins 0
RAD21 protein, human 0

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : European Research Council (ERC)
ID : Stg 85222 "PreventALL"
Organisme : ERA Per Med
ID : JTC 2018 "GEPARD"
Organisme : German Cancer Aid
ID : 70114539
Organisme : Italian Association for Cancer Research
ID : IG2018 n.21999
Organisme : Deutsche Forschungsgemeinschaft
ID : JE150/31-1

Références

Curr Biol. 2010 May 25;20(10):957-63
pubmed: 20451387
Hum Mol Genet. 2009 Feb 1;18(3):418-27
pubmed: 18996922
Cell. 2017 Jul 27;170(3):507-521.e18
pubmed: 28735753
Genome Biol. 2014;15(12):550
pubmed: 25516281
Cell. 2012 Aug 31;150(5):961-74
pubmed: 22901742
Cell. 2013 Aug 15;154(4):801-13
pubmed: 23953112
Science. 2000 May 26;288(5470):1379-85
pubmed: 10827941
Curr Protoc. 2021 Mar;1(3):e90
pubmed: 33780170
Nature. 1999 Jul 1;400(6739):37-42
pubmed: 10403247
Pediatr Blood Cancer. 2022 Jan;69(1):e29361
pubmed: 34597466
Nat Rev Mol Cell Biol. 2016 Jul;17(7):399-412
pubmed: 27075410
Cell. 2008 Feb 8;132(3):422-33
pubmed: 18237772
Cell. 2017 Oct 5;171(2):305-320.e24
pubmed: 28985562
Bioinformatics. 2014 Apr 1;30(7):923-30
pubmed: 24227677
Annu Rev Genomics Hum Genet. 2016 Aug 31;17:17-43
pubmed: 27089971
Proc Natl Acad Sci U S A. 2011 Jun 7;108(23):9566-71
pubmed: 21606361
Cell. 1997 Oct 3;91(1):47-57
pubmed: 9335334
J Exp Med. 2015 Oct 19;212(11):1833-50
pubmed: 26438359
Nat Commun. 2020 Dec 2;11(1):6178
pubmed: 33268790
Cell. 1997 Oct 3;91(1):35-45
pubmed: 9335333
Nat Rev Cancer. 2020 Sep;20(9):504-515
pubmed: 32514055
Eur J Hum Genet. 2021 Aug;29(8):1301-1311
pubmed: 33840814
Bioinformatics. 2010 Apr 1;26(7):873-81
pubmed: 20147302
Eur J Cancer. 2016 Sep;65:91-101
pubmed: 27479119
Nat Genet. 2013 Oct;45(10):1232-7
pubmed: 23955599
Genes Dev. 1998 Jul 1;12(13):1986-97
pubmed: 9649503
Gene. 2020 Oct 20;758:144966
pubmed: 32687945
Leukemia. 2012 May;26(5):963-71
pubmed: 22289921
Hum Genet. 2020 May;139(5):575-592
pubmed: 32193685
Cell Stem Cell. 2015 Dec 3;17(6):675-688
pubmed: 26607380
ACS Chem Biol. 2007 Jun 15;2(6):399-407
pubmed: 17530733
Curr Biol. 2001 Jun 26;11(12):991-5
pubmed: 11448778
Front Genet. 2012 Sep 12;3:171
pubmed: 22988450
PLoS One. 2010 Aug 12;5(8):e12112
pubmed: 20711430
Nat Immunol. 2021 Feb;22(2):240-253
pubmed: 33432228
Nature. 2008 Feb 14;451(7180):796-801
pubmed: 18235444
Crit Rev Oncol Hematol. 2009 Dec;72(3):181-93
pubmed: 19162508
Int J Radiat Oncol Biol Phys. 2001 Aug 1;50(5):1323-31
pubmed: 11483345
J Clin Pathol. 2019 Aug;72(8):558-561
pubmed: 30948435
Mol Cell. 2002 Apr;9(4):773-88
pubmed: 11983169
J Hematol Oncol. 2022 Jan 22;15(1):10
pubmed: 35065680
Nature. 2013 Sep 26;501(7468):564-8
pubmed: 23975099
Cold Spring Harb Perspect Med. 2016 Dec 1;6(12):
pubmed: 27742736
Haematologica. 2021 Aug 01;106(8):2215-2223
pubmed: 32675227
Proc Natl Acad Sci U S A. 2014 Jan 21;111(3):996-1001
pubmed: 24335803
Nature. 2017 Apr 27;544(7651):503-507
pubmed: 28424523
Genes Chromosomes Cancer. 2021 Jun;60(6):410-417
pubmed: 33368842
Int J Cancer. 2017 Sep 1;141(5):877-886
pubmed: 28597939
J Cell Sci. 2005 May 15;118(Pt 10):2133-41
pubmed: 15855230
Hum Mol Genet. 2007 Jun 15;16(12):1478-87
pubmed: 17468178
Nat Cell Biol. 2000 Aug;2(8):492-9
pubmed: 10934469
Nature. 2011 Aug 10;476(7361):467-71
pubmed: 21832993

Auteurs

Anne Schedel (A)

Pediatric Hematology and Oncology, Department of Pediatrics, University Hospital Carl Gustav Carus, TU Dresden, 01307 Dresden, Germany.

Ulrike Anne Friedrich (UA)

Pediatric Hematology and Oncology, Department of Pediatrics, University Hospital Carl Gustav Carus, TU Dresden, 01307 Dresden, Germany.

Mina N F Morcos (MNF)

Department of Pediatrics, School of Medicine, Technical University of Munich; 80804 Munich, Germany.

Rabea Wagener (R)

Department of Pediatric Oncology, Hematology and Clinical Immunology, Heinrich-Heine University Duesseldorf, Medical Faculty, 40225 Duesseldorf, Germany.

Juha Mehtonen (J)

Institute of Biomedicine, School of Medicine, University of Eastern Finland, Yliopistonranta 1, FI-70211 Kuopio, Finland.

Titus Watrin (T)

Department of Pediatric Oncology, Hematology and Clinical Immunology, Heinrich-Heine University Duesseldorf, Medical Faculty, 40225 Duesseldorf, Germany.

Claudia Saitta (C)

Tettamanti Research Center, Pediatrics, University of Milan Bicocca, Fondazione MBBM/San Gerardo Hospital, 20900 Monza, Italy.

Triantafyllia Brozou (T)

Department of Pediatric Oncology, Hematology and Clinical Immunology, Heinrich-Heine University Duesseldorf, Medical Faculty, 40225 Duesseldorf, Germany.

Pia Michler (P)

Pediatric Hematology and Oncology, Department of Pediatrics, University Hospital Carl Gustav Carus, TU Dresden, 01307 Dresden, Germany.

Carolin Walter (C)

Institute of Medical Informatics, University of Muenster, 48149 Muenster, Germany.

Asta Försti (A)

Division of Pediatric Neurooncology, German Cancer Research Center (DKFZ), German Cancer Consortium (DKTK), 69120 Heidelberg, Germany.
Hopp Children's Cancer Center Heidelberg (KiTZ), 69120 Heidelberg, Germany.

Arka Baksi (A)

Institute of Physiological Chemistry, Medical Faculty Carl Gustav Carus, TU Dresden, 01307 Dresden, Germany.

Maria Menzel (M)

Pediatric Hematology and Oncology, Department of Pediatrics, University Hospital Carl Gustav Carus, TU Dresden, 01307 Dresden, Germany.

Peter Horak (P)

Division of Translational Medical Oncology, National Center for Tumor Diseases (NCT) and German Cancer Research Center (DKFZ), 69120 Heidelberg, Germany.

Nagarajan Paramasivam (N)

Computational Oncology, Molecular Diagnostics Program, National Center for Tumor Diseases (NCT), 69120 Heidelberg, Germany.

Grazia Fazio (G)

Tettamanti Research Center, Pediatrics, University of Milan Bicocca, Fondazione MBBM/San Gerardo Hospital, 20900 Monza, Italy.

Robert J Autry (RJ)

Division of Pediatric Neurooncology, German Cancer Research Center (DKFZ), German Cancer Consortium (DKTK), 69120 Heidelberg, Germany.
Hopp Children's Cancer Center Heidelberg (KiTZ), 69120 Heidelberg, Germany.

Stefan Fröhling (S)

Division of Translational Medical Oncology, National Center for Tumor Diseases (NCT) and German Cancer Research Center (DKFZ), 69120 Heidelberg, Germany.

Meinolf Suttorp (M)

Pediatric Hematology and Oncology, Department of Pediatrics, University Hospital Carl Gustav Carus, TU Dresden, 01307 Dresden, Germany.

Christoph Gertzen (C)

Institute for Pharmaceutical and Medicinal Chemistry, Heinrich-Heine-Universität Duesseldorf, Universitätsstraße 1, 40225 Duesseldorf, Germany.

Holger Gohlke (H)

Institute for Pharmaceutical and Medicinal Chemistry, Heinrich-Heine-Universität Duesseldorf, Universitätsstraße 1, 40225 Duesseldorf, Germany.
John von Neumann Institute for Computing (NIC), Jülich Supercomputing Centre (JSC), Institute of Biological Information Processing (IBI-7: Structural Biochemistry), Forschungszentrum Jülich GmbH, 52425 Jülich, Germany.

Sanil Bhatia (S)

Department of Pediatric Oncology, Hematology and Clinical Immunology, Heinrich-Heine University Duesseldorf, Medical Faculty, 40225 Duesseldorf, Germany.

Karin Wadt (K)

Department of Clinical Genetics, University Hospital of Copenhagen, Faculty of health and Medical Sciences, University of Copenhagen, 2100 Copenhagen, Denmark.

Kjeld Schmiegelow (K)

Department of Paediatrics and Adolescent Medicine, Copenhagen University Hospital Rigshospitalet, 2100 Copenhagen, Denmark.

Martin Dugas (M)

Institute of Medical Informatics, University of Muenster, 48149 Muenster, Germany.
Institute of Medical Informatics, Heidelberg University Hospital, 69120 Heidelberg, Germany.

Daniela Richter (D)

Department of Translational Medical Oncology, National Center for Tumor Diseases (NCT) Dresden, 01307 Dresden, Germany.
German Cancer Consortium (DKTK), 01307 Dresden, Germany.

Hanno Glimm (H)

Department of Translational Medical Oncology, National Center for Tumor Diseases (NCT) Dresden, 01307 Dresden, Germany.
German Cancer Consortium (DKTK), 01307 Dresden, Germany.
Translational Functional Cancer Genomics, National Center for Tumor Diseases (NCT) and German Cancer Research Center (DKFZ), 69120 Heidelberg, Germany.

Merja Heinäniemi (M)

Institute of Biomedicine, School of Medicine, University of Eastern Finland, Yliopistonranta 1, FI-70211 Kuopio, Finland.

Rolf Jessberger (R)

Institute of Physiological Chemistry, Medical Faculty Carl Gustav Carus, TU Dresden, 01307 Dresden, Germany.

Gianni Cazzaniga (G)

Tettamanti Research Center, Pediatrics, University of Milan Bicocca, Fondazione MBBM/San Gerardo Hospital, 20900 Monza, Italy.
Medical Genetics, Department of Medicine and Surgery, University of Milan Bicocca, 20900 Monza, Italy.

Arndt Borkhardt (A)

Department of Pediatric Oncology, Hematology and Clinical Immunology, Heinrich-Heine University Duesseldorf, Medical Faculty, 40225 Duesseldorf, Germany.

Julia Hauer (J)

Department of Pediatrics, School of Medicine, Technical University of Munich; 80804 Munich, Germany.
German Cancer Consortium (DKTK), 81675 Munich, Germany.

Franziska Auer (F)

Department of Pediatrics, School of Medicine, Technical University of Munich; 80804 Munich, Germany.

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Classifications MeSH