A Case Report of Behcet's Disease With Thromboses in the Superior Vena Cava and External Iliac Vein.

autoimmune disease behcet's disease behcet's syndrome cardiovascular disease mucocutaneous ulcers pathergy superior vena cava (svc) syndrome thromboembolic disease thrombotic angiopathy

Journal

Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737

Informations de publication

Date de publication:
Apr 2022
Historique:
accepted: 12 04 2022
entrez: 16 5 2022
pubmed: 17 5 2022
medline: 17 5 2022
Statut: epublish

Résumé

Behcet's disease (BD), also known as Behcet's syndrome, is a rare, chronic, autoimmune disorder of unknown origin. Its manifestations are thought to be caused by vasculitis, resulting in damage to blood vessels of all sizes throughout the body. We report a 25-year-old Pakistani male who is sexually active and presents with a one-year history of shortness of breath, cough, exertional dyspnea, and neck and facial swelling. On examination, he had severe anemia, mouth ulcers, distended neck and chest veins, prominent abdominal veins, and a scrotal ulcer. After going through mandatory investigations to evaluate the presenting signs and symptoms, thromboses were found in the major veins, including the superior vena cava (SVC) and external iliac vein, as well as a positive pathergy test. Accordingly, a diagnosis of Behcet's disease with cardiomyopathy and venous thrombosis was made. He was treated with anticoagulants, steroids, and azathioprine for six months and subsequently went into remission.

Identifiants

pubmed: 35573561
doi: 10.7759/cureus.24064
pmc: PMC9097467
doi:

Types de publication

Case Reports

Langues

eng

Pagination

e24064

Informations de copyright

Copyright © 2022, Sayeed et al.

Déclaration de conflit d'intérêts

The authors have declared that no competing interests exist.

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Auteurs

Faiza Zafar Sayeed (FZ)

Department of Internal Medicine, Dr. Ruth K. M. Pfau Civil Hospital Karachi, Karachi, PAK.

Muhammad Nashit (M)

Department of Internal Medicine, Dr. Ruth K. M. Pfau Civil Hospital Karachi, Karachi, PAK.

Shaheen Bhatty (S)

Department of Internal Medicine, Dr. Ruth K. M. Pfau Civil Hospital Karachi, Karachi, PAK.

Bushra Z Sayeed (BZ)

Department of Internal Medicine, Dr. Ruth K. M. Pfau Civil Hospital Karachi, Karachi, PAK.

Fariha Asad (F)

Department of Internal Medicine, Dr. Ruth K. M. Pfau Civil Hospital Karachi, Karachi, PAK.

Classifications MeSH