A Case Report of Behcet's Disease With Thromboses in the Superior Vena Cava and External Iliac Vein.
autoimmune disease
behcet's disease
behcet's syndrome
cardiovascular disease
mucocutaneous ulcers
pathergy
superior vena cava (svc) syndrome
thromboembolic disease
thrombotic angiopathy
Journal
Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737
Informations de publication
Date de publication:
Apr 2022
Apr 2022
Historique:
accepted:
12
04
2022
entrez:
16
5
2022
pubmed:
17
5
2022
medline:
17
5
2022
Statut:
epublish
Résumé
Behcet's disease (BD), also known as Behcet's syndrome, is a rare, chronic, autoimmune disorder of unknown origin. Its manifestations are thought to be caused by vasculitis, resulting in damage to blood vessels of all sizes throughout the body. We report a 25-year-old Pakistani male who is sexually active and presents with a one-year history of shortness of breath, cough, exertional dyspnea, and neck and facial swelling. On examination, he had severe anemia, mouth ulcers, distended neck and chest veins, prominent abdominal veins, and a scrotal ulcer. After going through mandatory investigations to evaluate the presenting signs and symptoms, thromboses were found in the major veins, including the superior vena cava (SVC) and external iliac vein, as well as a positive pathergy test. Accordingly, a diagnosis of Behcet's disease with cardiomyopathy and venous thrombosis was made. He was treated with anticoagulants, steroids, and azathioprine for six months and subsequently went into remission.
Identifiants
pubmed: 35573561
doi: 10.7759/cureus.24064
pmc: PMC9097467
doi:
Types de publication
Case Reports
Langues
eng
Pagination
e24064Informations de copyright
Copyright © 2022, Sayeed et al.
Déclaration de conflit d'intérêts
The authors have declared that no competing interests exist.
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