Fahr syndrome discovered in adulthood revealing a rare

Albright's hereditary osteodystrophy Fahr syndrome GNAS mutation molecular analysis pseudohypoparathyroidism

Journal

Clinical case reports
ISSN: 2050-0904
Titre abrégé: Clin Case Rep
Pays: England
ID NLM: 101620385

Informations de publication

Date de publication:
May 2022
Historique:
received: 13 03 2022
revised: 26 04 2022
accepted: 27 04 2022
entrez: 23 5 2022
pubmed: 24 5 2022
medline: 24 5 2022
Statut: epublish

Résumé

Pseudohypoparathyroidism (PHP) indicates a rare heterogeneous group of disorders characterized by hypocalcemia, hyperphosphatemia, increased serum concentration of parathyroid hormone (PTH), and insensitivity to the biologic activity of PTH. One of its most common types is PHP-1a. In this report, we present a familial PHP-1a and a novel mutation of the

Identifiants

pubmed: 35600030
doi: 10.1002/ccr3.5849
pii: CCR35849
pmc: PMC9109644
doi:

Types de publication

Case Reports

Langues

eng

Pagination

e05849

Informations de copyright

© 2022 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd.

Déclaration de conflit d'intérêts

The authors declare no conflicts of interest.

Références

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Auteurs

Wided Debbabi (W)

Department of Endocrinology Faculty of Medicine of Sousse Ibn Jazzar University Hospital Kairouan University of Medicine Kairouan Tunisia.

Dayssem Khelifi (D)

Department of Endocrinology Faculty of Medicine of Sousse Ibn Jazzar University Hospital Kairouan University of Medicine Kairouan Tunisia.

Issam Kharrat (I)

Department of Endocrinology Faculty of Medicine of Sousse Ibn Jazzar University Hospital Kairouan University of Medicine Kairouan Tunisia.

Slim Samet (S)

Department of Endocrinology Faculty of Medicine of Sousse Ibn Jazzar University Hospital Kairouan University of Medicine Kairouan Tunisia.

Classifications MeSH