Urachal rhabdomyosarcoma: A case report of an extremely rare localisation.
Oncology
Pediatrics
Rhabdomyosarcoma (RMS)
Urachus
Journal
Urology case reports
ISSN: 2214-4420
Titre abrégé: Urol Case Rep
Pays: United States
ID NLM: 101626357
Informations de publication
Date de publication:
Jul 2022
Jul 2022
Historique:
received:
27
03
2022
revised:
26
04
2022
accepted:
04
05
2022
entrez:
23
5
2022
pubmed:
24
5
2022
medline:
24
5
2022
Statut:
epublish
Résumé
Urachus is a tubular structure connecting the allatois to the bladder's apex, in the embryonic development. We report a rare case of a 5-year-old boy, with no past medical history, complaining of secondary enuresis, pollakiuria and urgent incontinence. Physical exam revealed a hypogastric mass. Echo guided percutaneous biopsy followed by a histological analysis showed embryonal RMS. The remainder of the staging ruled out metastasis. The patient received neoadjuvant chemotherapy before proceeding to complete tumor excision. Surgical exploration revealed that the tumor was primitively related to the urachus. Total resection was performed. The one year follow-up was uneventful.
Identifiants
pubmed: 35600805
doi: 10.1016/j.eucr.2022.102109
pii: S2214-4420(22)00121-8
pmc: PMC9121247
doi:
Types de publication
Case Reports
Langues
eng
Pagination
102109Informations de copyright
© 2022 The Authors.
Déclaration de conflit d'intérêts
The authors declare that there are no conflicts of interest regarding the publication of this article.
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