Identifying Features of Cardiac Disease Phenotypes Based on Mechanical Function in a Catecholaminergic Polymorphic Ventricular Tachycardia Model.

2D cell culture DIC contraction rate disease model iPSC-cardiomyocytes mechanical strain microcontact printing

Journal

Frontiers in bioengineering and biotechnology
ISSN: 2296-4185
Titre abrégé: Front Bioeng Biotechnol
Pays: Switzerland
ID NLM: 101632513

Informations de publication

Date de publication:
2022
Historique:
received: 10 02 2022
accepted: 12 04 2022
entrez: 27 5 2022
pubmed: 28 5 2022
medline: 28 5 2022
Statut: epublish

Résumé

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is characterized by an arrhythmogenic mechanism involving disruption of calcium handling. This genetic disease can lead to sudden death in children and young adults during physical or emotional stress. Prior CPVT studies have focused on calcium handling, but mechanical functionality has rarely been investigated

Identifiants

pubmed: 35620470
doi: 10.3389/fbioe.2022.873531
pii: 873531
pmc: PMC9127198
doi:

Types de publication

Journal Article

Langues

eng

Pagination

873531

Subventions

Organisme : NHLBI NIH HHS
ID : R01 HL055438
Pays : United States
Organisme : NHLBI NIH HHS
ID : R01 HL139738
Pays : United States

Informations de copyright

Copyright © 2022 Stempien, Josvai, de Lange, Hernandez, Notbohm, Kamp, Valdivia, Eckhardt, Maginot, Ralphe and Crone.

Déclaration de conflit d'intérêts

TK was a consultant for Cellular Dynamics International, a stem cell biotechnology company. The remaining authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

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Auteurs

A Stempien (A)

Department of Biomedical Engineering, University of Wisconsin-Madison, Madison, WI, United States.
Wisconsin Institute for Discovery, University of Wisconsin-Madison, Madison, WI, United States.

M Josvai (M)

Department of Biomedical Engineering, University of Wisconsin-Madison, Madison, WI, United States.
Wisconsin Institute for Discovery, University of Wisconsin-Madison, Madison, WI, United States.

W J de Lange (WJ)

Department of Pediatrics, University of Wisconsin School of Medicine and Public Health, Madison, WI, United States.

J J Hernandez (JJ)

Department of Pediatrics, University of Wisconsin School of Medicine and Public Health, Madison, WI, United States.

J Notbohm (J)

Department of Engineering Physics, University of Wisconsin-Madison, Madison, WI, United States.

T J Kamp (TJ)

Department of Medicine, Division of Cardiovascular Medicine, University of Wisconsin-Madison, Madison, WI, United States.
Department of Cell and Regenerative Biology, University of Wisconsin-Madison, Madison, WI, United States.
Cellular and Molecular Arrhythmia Research Program, Department of Medicine, University of Wisconsin-Madison, Madison, WI, United States.

H H Valdivia (HH)

Department of Medicine, Division of Cardiovascular Medicine, University of Wisconsin-Madison, Madison, WI, United States.

L L Eckhardt (LL)

Department of Medicine, Division of Cardiovascular Medicine, University of Wisconsin-Madison, Madison, WI, United States.
Cellular and Molecular Arrhythmia Research Program, Department of Medicine, University of Wisconsin-Madison, Madison, WI, United States.

K R Maginot (KR)

Department of Pediatrics, University of Wisconsin School of Medicine and Public Health, Madison, WI, United States.

J C Ralphe (JC)

Department of Pediatrics, University of Wisconsin School of Medicine and Public Health, Madison, WI, United States.

W C Crone (WC)

Department of Biomedical Engineering, University of Wisconsin-Madison, Madison, WI, United States.
Wisconsin Institute for Discovery, University of Wisconsin-Madison, Madison, WI, United States.
Department of Engineering Physics, University of Wisconsin-Madison, Madison, WI, United States.

Classifications MeSH