Co-Occurrence of Multiple Sclerosis and Amyotrophic Lateral Sclerosis in an FUS-Mutated Patient: A Case Report.

FUS amyotrophic lateral sclerosis clinical neurophysiology multiple sclerosis oligodendroglial dysfunction

Journal

Brain sciences
ISSN: 2076-3425
Titre abrégé: Brain Sci
Pays: Switzerland
ID NLM: 101598646

Informations de publication

Date de publication:
21 Apr 2022
Historique:
received: 02 03 2022
revised: 09 04 2022
accepted: 19 04 2022
entrez: 28 5 2022
pubmed: 29 5 2022
medline: 29 5 2022
Statut: epublish

Résumé

A concomitant presentation of relapsing remitting multiple sclerosis (RRMS) and amyotrophic lateral sclerosis (ALS) is quite rare. However, a review of the literature showed an increased co-occurrence of both diseases, including in genetically determined cases. We report the case of a 49-year-old woman with a history of RRMS who developed a progressive subacute loss of strength in her left arm. The patient’s father died from ALS, and her paternal uncle had Parkinson’s disease. Brain and cervical MRIs were performed, and new demyelinating lesions were excluded. Electromyography (EMG) of the upper limbs showed fibrillations and fasciculations in distal muscles of both arms. In the following months, the patient presented a progressive loss of strength in the proximal and distal muscles of the right arm and hyperreflexia in the lower limbs. EMG and central motor conduction were consistent with ALS. A genetic test was carried out, revealing a mutation in the FUS gene (exon 15; c. 1562 G>A). To our knowledge, the co-occurrence of MS and ALS in patients with FUS mutation is extremely rare. We hypothesize a common pathway for both diseases based on the possibility of a shared oligodendroglial dysfunction due to FUS mutation.

Identifiants

pubmed: 35624917
pii: brainsci12050531
doi: 10.3390/brainsci12050531
pmc: PMC9139033
pii:
doi:

Types de publication

Case Reports

Langues

eng

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Auteurs

Luigi Fiondella (L)

Neurology Unit, Neuromotor and Rehabilitation Department, AUSL-IRCCS of Reggio Emilia, 42123 Reggio Emilia, Italy.
Department of Biomedical, Metabolic and Neural Sciences, University of Modena and Reggio Emilia, 41125 Modena, Italy.

Francesco Cavallieri (F)

Neurology Unit, Neuromotor and Rehabilitation Department, AUSL-IRCCS of Reggio Emilia, 42123 Reggio Emilia, Italy.
Clinical and Experimental Medicine PhD Program, University of Modena and Reggio Emilia, 41125 Modena, Italy.

Elena Canali (E)

Neurology Unit, Neuromotor and Rehabilitation Department, AUSL-IRCCS of Reggio Emilia, 42123 Reggio Emilia, Italy.

Maria Paola Cabboi (MP)

Neurology Unit, Neuromotor and Rehabilitation Department, AUSL-IRCCS of Reggio Emilia, 42123 Reggio Emilia, Italy.

Alessandro Marti (A)

Neurology Unit, Neuromotor and Rehabilitation Department, AUSL-IRCCS of Reggio Emilia, 42123 Reggio Emilia, Italy.

Francesca Sireci (F)

Neurology Unit, Neuromotor and Rehabilitation Department, AUSL-IRCCS of Reggio Emilia, 42123 Reggio Emilia, Italy.

Alena Fiocchi (A)

Physical Medicine and Rehabilitation Unit, AUSL-IRCCS of Reggio Emilia, 42123 Reggio Emilia, Italy.

Gloria Montanari (G)

Pneumology Unit, AUSL-IRCCS of Reggio Emilia, 42123 Reggio Emilia, Italy.

Sara Montepietra (S)

Neurology Unit, Neuromotor and Rehabilitation Department, AUSL-IRCCS of Reggio Emilia, 42123 Reggio Emilia, Italy.

Franco Valzania (F)

Neurology Unit, Neuromotor and Rehabilitation Department, AUSL-IRCCS of Reggio Emilia, 42123 Reggio Emilia, Italy.

Classifications MeSH