Total Colonic Aganglionosis in Hirschsprung disease.

Total Colonic Hirschsprung disease

Journal

Seminars in pediatric surgery
ISSN: 1532-9453
Titre abrégé: Semin Pediatr Surg
Pays: United States
ID NLM: 9216162

Informations de publication

Date de publication:
Apr 2022
Historique:
entrez: 11 6 2022
pubmed: 12 6 2022
medline: 15 6 2022
Statut: ppublish

Résumé

Total Colonic Hirschsprung Disease (HD) can be challenging from a diagnostic and management standpoint and occurs in around 8% of cases of HD. Long term outcomes are difficult to compare due to variation in length of aganglionosis, chosen surgical techniques, and terminology utilized in the literature. In this review we highlight some of the management controversies and clinical challenges and emphasize future areas of suggested collaboration and research.

Identifiants

pubmed: 35690465
pii: S1055-8586(22)00026-9
doi: 10.1016/j.sempedsurg.2022.151165
pii:
doi:

Types de publication

Journal Article Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

151165

Informations de copyright

Copyright © 2022 Elsevier Inc. All rights reserved.

Auteurs

Richard J Wood (RJ)

Department of Pediatric Colorectal and Pelvic Reconstructive Surgery, Nationwide Children's Hospital, Columbus, OH, USA. Electronic address: Richard.Wood@nationwidechildrens.org.

Aaron P Garrison (AP)

Division of Pediatric General and Thoracic Surgery, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.

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Classifications MeSH