Diagnosing Alström syndrome in a patient followed up with syndromic obesity for years.

ALMS1 gene biallelic mutations obesity rare diseases

Journal

Intractable & rare diseases research
ISSN: 2186-3644
Titre abrégé: Intractable Rare Dis Res
Pays: Japan
ID NLM: 101586847

Informations de publication

Date de publication:
May 2022
Historique:
received: 10 02 2022
revised: 13 04 2022
accepted: 20 04 2022
entrez: 15 6 2022
pubmed: 16 6 2022
medline: 16 6 2022
Statut: ppublish

Résumé

Alström syndrome (AS) is a rare autosomal recessive monogenic disorder caused by mutations of the

Identifiants

pubmed: 35702577
doi: 10.5582/irdr.2022.01024
pmc: PMC9161128
doi:

Types de publication

Journal Article

Langues

eng

Pagination

84-86

Informations de copyright

2022, International Research and Cooperation Association for Bio & Socio - Sciences Advancement.

Déclaration de conflit d'intérêts

The authors have no conflicts of interest to disclose.

Références

Nat Genet. 2002 May;31(1):74-8
pubmed: 11941369
Eur J Hum Genet. 2007 Dec;15(12):1193-202
pubmed: 17940554

Auteurs

Mustafa Yakubi (M)

Department of Medical Genetics, Faculty of Medicine, Erciyes University, Kayseri, Turkey.

Dilek Cicek (D)

Department of Pediatrics, Faculty of Medicine, Erciyes University, Kayseri, Turkey.

Mikail Demir (M)

Department of Medical Genetics, Faculty of Medicine, Erciyes University, Kayseri, Turkey.

Abdulbaki Yildirim (A)

Department of Medical Genetics, Faculty of Medicine, Erciyes University, Kayseri, Turkey.

Nihal Hatipoglu (N)

Department of Pediatrics, Faculty of Medicine, Erciyes University, Kayseri, Turkey.

Yusuf Ozkul (Y)

Department of Medical Genetics, Faculty of Medicine, Erciyes University, Kayseri, Turkey.

Munis Dundar (M)

Department of Medical Genetics, Faculty of Medicine, Erciyes University, Kayseri, Turkey.

Classifications MeSH