Selenium Status in Paediatric Patients with Neurodevelopmental Diseases.


Journal

Nutrients
ISSN: 2072-6643
Titre abrégé: Nutrients
Pays: Switzerland
ID NLM: 101521595

Informations de publication

Date de publication:
08 Jun 2022
Historique:
received: 13 05 2022
revised: 03 06 2022
accepted: 06 06 2022
entrez: 24 6 2022
pubmed: 25 6 2022
medline: 28 6 2022
Statut: epublish

Résumé

Neurodevelopmental diseases are often associated with other comorbidities, especially inflammatory processes. The disease may affect the trace element (TE) status, which in turn may affect disease severity and progression. Selenium (Se) is an essential TE required for the biosynthesis of selenoproteins including the transporter selenoprotein P (SELENOP) and extracellular glutathione peroxidase (GPX3). SELENOP deficiency in transgenic mice resulted in a Se status-dependent phenotype characterized by impaired growth and disturbed neuronal development, with epileptic seizures on a Se-deficient diet. Therefore, we hypothesized that Se and SELENOP deficiencies may be prevalent in paediatric patients with a neurodevelopmental disease. In an exploratory cross-sectional study, serum samples from children with neurodevelopmental diseases (

Identifiants

pubmed: 35745104
pii: nu14122375
doi: 10.3390/nu14122375
pmc: PMC9227519
pii:
doi:

Substances chimiques

Selenoprotein P 0
Selenoproteins 0
Trace Elements 0
Glutathione Peroxidase EC 1.11.1.9
Selenium H6241UJ22B

Types de publication

Journal Article Observational Study

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : Deutsche Forschungsgemeinschaft
ID : CRC/TR 296 "Local control of TH action" (LocoTact, P17)
Organisme : Deutsche Forschungsgemeinschaft
ID : Research Unit FOR-2558 "TraceAge" (Scho 849/6-2)

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Auteurs

Christian L Görlich (CL)

Institute for Experimental Endocrinology, Charité-Universitätsmedizin Berlin, 13353 Berlin, Germany.
Center for Chronically Sick Children (SPZ), Charité-Universitätsmedizin Berlin, 13353 Berlin, Germany.

Qian Sun (Q)

Institute for Experimental Endocrinology, Charité-Universitätsmedizin Berlin, 13353 Berlin, Germany.

Viola Roggenkamp (V)

Center for Chronically Sick Children (SPZ), Charité-Universitätsmedizin Berlin, 13353 Berlin, Germany.

Julian Hackler (J)

Institute for Experimental Endocrinology, Charité-Universitätsmedizin Berlin, 13353 Berlin, Germany.

Sebastian Mehl (S)

Institute for Experimental Endocrinology, Charité-Universitätsmedizin Berlin, 13353 Berlin, Germany.

Waldemar B Minich (WB)

Institute for Experimental Endocrinology, Charité-Universitätsmedizin Berlin, 13353 Berlin, Germany.

Angela M Kaindl (AM)

Center for Chronically Sick Children (SPZ), Charité-Universitätsmedizin Berlin, 13353 Berlin, Germany.
Department of Pediatric Neurology, Charité-Universitätsmedizin Berlin, 13353 Berlin, Germany.
Institute of Cell Biology and Neurobiology, Charité-Universitätsmedizin Berlin, 13353 Berlin, Germany.

Lutz Schomburg (L)

Institute for Experimental Endocrinology, Charité-Universitätsmedizin Berlin, 13353 Berlin, Germany.

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Classifications MeSH