Definition, diagnosis and clinical management of non-obstructive kidney dysplasia: a consensus statement by the ERKNet Working Group on Kidney Malformations.

chronic renal failure chronic renal insufficiency guidelines pediatrics ultrasonography

Journal

Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association
ISSN: 1460-2385
Titre abrégé: Nephrol Dial Transplant
Pays: England
ID NLM: 8706402

Informations de publication

Date de publication:
23 11 2022
Historique:
received: 28 02 2022
pubmed: 1 7 2022
medline: 25 11 2022
entrez: 30 6 2022
Statut: ppublish

Résumé

Kidney dysplasia is one of the most frequent causes of chronic kidney failure in children. While dysplasia is a histological diagnosis, the term 'kidney dysplasia' is frequently used in daily clinical life without histopathological confirmation. Clinical parameters of kidney dysplasia have not been clearly defined, leading to imprecise communication amongst healthcare professionals and patients. This lack of consensus hampers precise disease understanding and the development of specific therapies. Based on a structured literature search, we here suggest a common basis for clinical, imaging, genetic, pathological and basic science aspects of non-obstructive kidney dysplasia associated with functional kidney impairment. We propose to accept hallmark sonographic findings as surrogate parameters defining a clinical diagnosis of dysplastic kidneys. We suggest differentiated clinical follow-up plans for children with kidney dysplasia and summarize established monogenic causes for non-obstructive kidney dysplasia. Finally, we point out and discuss research gaps in the field.

Identifiants

pubmed: 35772019
pii: 6623684
doi: 10.1093/ndt/gfac207
pmc: PMC9681917
doi:

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

2351-2362

Subventions

Organisme : Medical Research Council
ID : MR/T016809/1
Pays : United Kingdom

Informations de copyright

© The Author(s) 2022. Published by Oxford University Press on behalf of the ERA.

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Auteurs

Stefan Kohl (S)

Department of Pediatrics, University Hospital of Cologne and Faculty of Medicine, University of Cologne, Cologne, Germany.

Fred E Avni (FE)

Department of Pediatric Imaging, Jeanne de Flandre Hospital, Lille University Hospitals, Lille Cedex, France.

Peter Boor (P)

Institute of Pathology, University Hospital RWTH Aachen, Aachen, Germany.
Medical Clinic II (Nephrology and Immunology), University Hospital RWTH Aachen, Aachen, Germany.

Valentina Capone (V)

Pediatric Nephrology, Dialysis and Transplant Unit, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, Milan, Italy.

William L Clapp (WL)

Department of Pathology, Immunology and Laboratory Medicine, University of Florida, Gainesville, FL, USA.

Diego De Palma (D)

Nuclear Medicine Unit, Circolo Hospital and Macchi Foundation, ASST-settelaghi, Varese, Italy.

Tess Harris (T)

The Polycystic Kidney Disease Charity, London, UK.

Laurence Heidet (L)

Laboratory of Hereditary Kidney Diseases, Université de Paris, Imagine Institute, INSERM UMR 1163, Paris, France.
APHP, Service de Néphrologie Pédiatrique, Centre de Référence MARHEA, Hôpital universitaire Necker-Enfants malades, Paris, France.

Alina C Hilger (AC)

Department of Pediatrics and Adolescent Medicine, Friedrich-Alexander University of Erlangen-Nürnberg, Erlangen, Germany.
Research Center On Rare Kidney Diseases (RECORD), University Hospital Erlangen, Erlangen, Germany.

Helen Liapis (H)

Nephrology Center, Ludwig Maximilian University (LMU), Munich, Germany.

Marc Lilien (M)

Department of Pediatric Nephrology, Wilhelmina Children's Hospital, University Medical Center Utrecht, Utrecht, The Netherlands.

Gianantonio Manzoni (G)

Pediatric Urology Unit, Fondazione IRCCS Cà Granda, Ospedale Maggiore Policlinico, Milan, Italy.

Giovanni Montini (G)

Pediatric Nephrology, Dialysis and Transplant Unit, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, Milan, Italy.
Department of Clinical Sciences and Community Health, University of Milano, Milan, Italy.

Susanna Negrisolo (S)

Laboratory of Immunopathology and Molecular Biology of the Kidney, Department of Women's and Children's Health, University of Padova, Padua, Italy.

Marie-Jeanne Pierrat (MJ)

Federation of European Patient Groups affected by Rare/Genetic Kidney Diseases (FEDERG), Brussels, Belgium.

Ann Raes (A)

Department of Pediatric Nephrology and Rheumatology, Ghent University Hospital, Ghent, Belgium.

Heiko Reutter (H)

Research Center On Rare Kidney Diseases (RECORD), University Hospital Erlangen, Erlangen, Germany.
Division of Neonatology and Pediatric Intensive Care Medicine, Department of Pediatric and Adolescent Medicine, Friedrich-Alexander-Universitat Erlangen-Nürnberg, Erlangen, Germany.

Michiel F Schreuder (MF)

Department of Pediatric Nephrology, Radboud University Medical Center, Radboud Institute for Molecular Life Sciences, Amalia Children's Hospital, Nijmegen, The Netherlands.

Stefanie Weber (S)

Department of Pediatric Nephrology, Marburg Kidney Research Center, Philipps University, Marburg, Germany.

Paul J D Winyard (PJD)

University College London Great Ormond Street, Institute of Child Health, London, UK.

Adrian S Woolf (AS)

Division of Cell Matrix Biology and Regenerative Medicine, School of Biological Sciences, Faculty of Biology Medicine and Health, University of Manchester, Manchester, UK.
Royal Manchester Children's Hospital, Manchester University National Health Service Foundation Trust, Manchester Academic Health Science Centre, Manchester, UK.

Franz Schaefer (F)

Division of Pediatric Nephrology, Center for Pediatrics and Adolescent Medicine, University Hospital Heidelberg, Heidelberg, Germany.

Max C Liebau (MC)

Department of Pediatrics, University Hospital of Cologne and Faculty of Medicine, University of Cologne, Cologne, Germany.
Center for Molecular Medicine Cologne, University Hospital of Cologne and Faculty of Medicine, University of Cologne, Cologne, Germany.
Center for Rare Diseases Cologne, University Hospital of Cologne and Faculty of Medicine, University of Cologne, Cologne, Germany.
Center for Family Health, University Hospital of Cologne and Faculty of Medicine, University of Cologne, Cologne, Germany.

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Classifications MeSH