Neuroimmune Dysregulation in Prepubertal and Adolescent Individuals Affected by Klinefelter Syndrome.


Journal

Endocrine, metabolic & immune disorders drug targets
ISSN: 2212-3873
Titre abrégé: Endocr Metab Immune Disord Drug Targets
Pays: United Arab Emirates
ID NLM: 101269157

Informations de publication

Date de publication:
2023
Historique:
received: 25 11 2021
revised: 31 03 2022
accepted: 01 04 2022
pubmed: 8 7 2022
medline: 10 3 2023
entrez: 7 7 2022
Statut: ppublish

Résumé

The syndrome Klinefelter syndrome (KS) is a genetic disorder due to an extra X chromosome in males. Many cases remain undiagnosed until the onset of major manifestations, which include hypergonadotropic hypogonadism and infertility. This condition is associated with many comorbidities that involve the cardiovascular, endocrine, and immune systems. Last but not the least, individuals with KS show a high risk of developing psychiatric and mood disorders in adult age. While many studies are accessible on KS in adult individuals, the neuroinflammatory condition in adolescent and prepubertal KS individuals is not fully known. Our study aims to evaluate in prepubertal and adolescent KS individuals, for the first time, the levels of the serum of brain-derived neurotrophic factor (BDNF), nerve growth factor (NGF), cytokines having subtle roles in oxidative processes, and neuroinflammation with respect to the levels of TNF-α, TGF-β, MCP-1, IL-1α, IL-2, IL-6, IL-10, and IL-12 and oxidative stress by employing free oxygen radicals defense and free oxygen radicals test. We found no changes in NGF and oxidative stress parameters, but BDNF decreased compared to healthy children. Quite interestingly, our data showed reduced levels of IL-2, IL-1α, IL- 12, IL-10, and IL-6 in prepubertal KS children. The present study discloses disrupted immune system and neurotrophin pathways in KS children.

Sections du résumé

BACKGROUND BACKGROUND
The syndrome Klinefelter syndrome (KS) is a genetic disorder due to an extra X chromosome in males. Many cases remain undiagnosed until the onset of major manifestations, which include hypergonadotropic hypogonadism and infertility. This condition is associated with many comorbidities that involve the cardiovascular, endocrine, and immune systems. Last but not the least, individuals with KS show a high risk of developing psychiatric and mood disorders in adult age.
OBJECTIVE OBJECTIVE
While many studies are accessible on KS in adult individuals, the neuroinflammatory condition in adolescent and prepubertal KS individuals is not fully known.
METHODS METHODS
Our study aims to evaluate in prepubertal and adolescent KS individuals, for the first time, the levels of the serum of brain-derived neurotrophic factor (BDNF), nerve growth factor (NGF), cytokines having subtle roles in oxidative processes, and neuroinflammation with respect to the levels of TNF-α, TGF-β, MCP-1, IL-1α, IL-2, IL-6, IL-10, and IL-12 and oxidative stress by employing free oxygen radicals defense and free oxygen radicals test.
RESULTS RESULTS
We found no changes in NGF and oxidative stress parameters, but BDNF decreased compared to healthy children. Quite interestingly, our data showed reduced levels of IL-2, IL-1α, IL- 12, IL-10, and IL-6 in prepubertal KS children.
CONCLUSION CONCLUSIONS
The present study discloses disrupted immune system and neurotrophin pathways in KS children.

Identifiants

pubmed: 35794745
pii: EMIDDT-EPUB-124968
doi: 10.2174/1871530322666220704101310
doi:

Substances chimiques

Interleukin-10 130068-27-8
Brain-Derived Neurotrophic Factor 0
Interleukin-2 0
Interleukin-6 0
Nerve Growth Factor 9061-61-4
Reactive Oxygen Species 0
Interleukin-12 187348-17-0

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

105-114

Informations de copyright

Copyright© Bentham Science Publishers; For any queries, please email at epub@benthamscience.net.

Auteurs

Luigi Tarani (L)

Department of Pediatrics, Sapienza University Hospital of Rome, Rome, Italy.

Flavio Maria Ceci (FM)

Department of Experimental Medicine, Sapienza University Hospital of Rome, Rome, Italy.

Valentina Carito (V)

Institute of Biochemistry and Cell Biology, Section of Neurobiology, National Research Council (IBBC-CNR), Rome, Italy.

Giampiero Ferraguti (G)

Department of Experimental Medicine, Sapienza University Hospital of Rome, Rome, Italy.

Carla Petrella (C)

Institute of Biochemistry and Cell Biology, Section of Neurobiology, National Research Council (IBBC-CNR), Rome, Italy.

Antonio Greco (A)

Department of Sense Organs, Sapienza University Hospital of Rome, Rome, Italy.

Massimo Ralli (M)

Department of Sense Organs, Sapienza University Hospital of Rome, Rome, Italy.

Antonio Minni (A)

Department of Sense Organs, Sapienza University Hospital of Rome, Rome, Italy.

Matteo Spaziani (M)

Department of Experimental Medicine, Section of Medical Pathophysiology, Food Science and Endocrinology, Sapienza University of Rome, Rome, Italy.

Andrea M Isidori (AM)

Department of Experimental Medicine, Section of Medical Pathophysiology, Food Science and Endocrinology, Sapienza University of Rome, Rome, Italy.

Maria Grazia Di Certo (MGD)

Institute of Biochemistry and Cell Biology, Section of Neurobiology, National Research Council (IBBC-CNR), Rome, Italy.

Christian Barbato (C)

Institute of Biochemistry and Cell Biology, Section of Neurobiology, National Research Council (IBBC-CNR), Rome, Italy.

Carolina Putotto (C)

Department of Pediatrics, Sapienza University Hospital of Rome, Rome, Italy.

Marco Fiore (M)

Institute of Biochemistry and Cell Biology, Section of Neurobiology, National Research Council (IBBC-CNR), Rome, Italy.

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Classifications MeSH