Lafora Disease and Alpha-Synucleinopathy in Two Adult Free-Ranging Moose (
Lafora disease
Lewy body
blindness
circling
moose
polyglucosan bodies
synucleinopathies
α-Synuclein
Journal
Animals : an open access journal from MDPI
ISSN: 2076-2615
Titre abrégé: Animals (Basel)
Pays: Switzerland
ID NLM: 101635614
Informations de publication
Date de publication:
25 Jun 2022
25 Jun 2022
Historique:
received:
30
05
2022
revised:
16
06
2022
accepted:
20
06
2022
entrez:
9
7
2022
pubmed:
10
7
2022
medline:
10
7
2022
Statut:
epublish
Résumé
Lafora disease is an autosomal recessive glycogen-storage disorder resulting from an accumulation of toxic polyglucosan bodies (PGBs) in the central nervous system, which causes behavioral and neurologic symptoms in humans and other animals. In this case study, brains collected from two young adult free-ranging moose (
Identifiants
pubmed: 35804532
pii: ani12131633
doi: 10.3390/ani12131633
pmc: PMC9264765
pii:
doi:
Types de publication
Journal Article
Langues
eng
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