The Clinical Spectrum and Disease Course of DRAM2 Retinopathy.

DRAM2 electrophysiology fundus autofluorescence imaging genetic spectrum genotype–phenotype correlation inherited retinal dystrophy phenotype variability

Journal

International journal of molecular sciences
ISSN: 1422-0067
Titre abrégé: Int J Mol Sci
Pays: Switzerland
ID NLM: 101092791

Informations de publication

Date de publication:
02 Jul 2022
Historique:
received: 31 05 2022
revised: 22 06 2022
accepted: 28 06 2022
entrez: 9 7 2022
pubmed: 10 7 2022
medline: 14 7 2022
Statut: epublish

Résumé

Pathogenic variants in DNA-damage regulated autophagy modulator 2 gene (

Identifiants

pubmed: 35806404
pii: ijms23137398
doi: 10.3390/ijms23137398
pmc: PMC9266529
pii:
doi:

Substances chimiques

DRAM2 protein, human 0
Membrane Proteins 0

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : Slovenian Research Agency
ID : ARRS J3-1750

Références

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Auteurs

Tjaša Krašovec (T)

Eye Hospital, University Medical Centre Ljubljana, Grablovičeva ulica 46, 1000 Ljubljana, Slovenia.

Marija Volk (M)

Clinical Institute of Medical Genetics, University Medical Centre Ljubljana, Šlajmajerjeva ulica 4, 1000 Ljubljana, Slovenia.

Maja Šuštar Habjan (M)

Eye Hospital, University Medical Centre Ljubljana, Grablovičeva ulica 46, 1000 Ljubljana, Slovenia.

Marko Hawlina (M)

Eye Hospital, University Medical Centre Ljubljana, Grablovičeva ulica 46, 1000 Ljubljana, Slovenia.
Faculty of Medicine, University of Ljubljana, Vrazov trg 2, 1000 Ljubljana, Slovenia.

Nataša Vidović Valentinčič (N)

Eye Hospital, University Medical Centre Ljubljana, Grablovičeva ulica 46, 1000 Ljubljana, Slovenia.
Faculty of Medicine, University of Ljubljana, Vrazov trg 2, 1000 Ljubljana, Slovenia.

Ana Fakin (A)

Eye Hospital, University Medical Centre Ljubljana, Grablovičeva ulica 46, 1000 Ljubljana, Slovenia.
Faculty of Medicine, University of Ljubljana, Vrazov trg 2, 1000 Ljubljana, Slovenia.

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Classifications MeSH