Lethal Congenital Contracture Syndrome 11: A Case Report and Literature Review.

GLDN arthrogryposis multiplex congenita fetal akinesia deformation sequence

Journal

Journal of clinical medicine
ISSN: 2077-0383
Titre abrégé: J Clin Med
Pays: Switzerland
ID NLM: 101606588

Informations de publication

Date de publication:
21 Jun 2022
Historique:
received: 17 05 2022
revised: 15 06 2022
accepted: 20 06 2022
entrez: 9 7 2022
pubmed: 10 7 2022
medline: 10 7 2022
Statut: epublish

Résumé

Lethal congenital contracture syndrome 11 (LCCS11) is caused by homozygous or compound heterozygous variants in the

Identifiants

pubmed: 35806855
pii: jcm11133570
doi: 10.3390/jcm11133570
pmc: PMC9267849
pii:
doi:

Types de publication

Case Reports

Langues

eng

Subventions

Organisme : Fundación Mutua Madrileña
ID : AP171442019
Organisme : AGAUR
ID : 2017SGR1134

Références

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Auteurs

Miriam Potrony (M)

Biochemistry and Molecular Genetics Department, Hospital Clinic of Barcelona, 08036 Barcelona, Spain.
CIBER of Rare Diseases (CIBERER), Instituto de Salud Carlos III, 28029 Madrid, Spain.
Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.

Antoni Borrell (A)

CIBER of Rare Diseases (CIBERER), Instituto de Salud Carlos III, 28029 Madrid, Spain.
BCNatal, Barcelona Center for Maternal-Fetal and Neonatal Medicine (Hospital Clínic and Hospital Sant Joan de Deu), Institut Clínic de Ginecologia, Obstetricia i Neonatologia Fetal i+D Fetal Medicine Research Center, Universitat de Barcelona, 08007 Barcelona, Spain.

Narcís Masoller (N)

CIBER of Rare Diseases (CIBERER), Instituto de Salud Carlos III, 28029 Madrid, Spain.
BCNatal, Barcelona Center for Maternal-Fetal and Neonatal Medicine (Hospital Clínic and Hospital Sant Joan de Deu), Institut Clínic de Ginecologia, Obstetricia i Neonatologia Fetal i+D Fetal Medicine Research Center, Universitat de Barcelona, 08007 Barcelona, Spain.

Alfons Nadal (A)

Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.
Pathology Department, Biomedical Diagnostic Center Hospital Clínic de Barcelona, 08036 Barcelona, Spain.
Department of Basic Clinical Practice, Medical School, Universitat de Barcelona, 08007 Barcelona, Spain.

Leonardo Rodriguez-Carunchio (L)

Pathology Department, Biomedical Diagnostic Center Hospital Clínic de Barcelona, 08036 Barcelona, Spain.
Medicine Department, University of Vic-Central University of Catalonia (UVic-UCC), 08500 Barcelona, Spain.

Karmele Saez de Gordoa Elizalde (K)

Pathology Department, Biomedical Diagnostic Center Hospital Clínic de Barcelona, 08036 Barcelona, Spain.

Juan Francisco Quesada-Espinosa (JF)

Genetics Department, 12 de Octubre University Hospital, 28041 Madrid, Spain.
UDISGEN (Unidad de Dismorfología y Genética), 12 de Octubre University Hospital, 28041 Madrid, Spain.

Jose Luis Villanueva-Cañas (JL)

Molecular Biology CORE (CDB), Hospital Clínic de Barcelona, 08036 Barcelona, Spain.

Montse Pauta (M)

Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.
BCNatal, Barcelona Center for Maternal-Fetal and Neonatal Medicine (Hospital Clínic and Hospital Sant Joan de Deu), Institut Clínic de Ginecologia, Obstetricia i Neonatologia Fetal i+D Fetal Medicine Research Center, Universitat de Barcelona, 08007 Barcelona, Spain.

Meritxell Jodar (M)

Biochemistry and Molecular Genetics Department, Hospital Clinic of Barcelona, 08036 Barcelona, Spain.
Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.

Irene Madrigal (I)

Biochemistry and Molecular Genetics Department, Hospital Clinic of Barcelona, 08036 Barcelona, Spain.
CIBER of Rare Diseases (CIBERER), Instituto de Salud Carlos III, 28029 Madrid, Spain.
Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.

Celia Badenas (C)

Biochemistry and Molecular Genetics Department, Hospital Clinic of Barcelona, 08036 Barcelona, Spain.
CIBER of Rare Diseases (CIBERER), Instituto de Salud Carlos III, 28029 Madrid, Spain.
Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.

Maria Isabel Alvarez-Mora (MI)

Biochemistry and Molecular Genetics Department, Hospital Clinic of Barcelona, 08036 Barcelona, Spain.
CIBER of Rare Diseases (CIBERER), Instituto de Salud Carlos III, 28029 Madrid, Spain.
Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.

Laia Rodriguez-Revenga (L)

Biochemistry and Molecular Genetics Department, Hospital Clinic of Barcelona, 08036 Barcelona, Spain.
CIBER of Rare Diseases (CIBERER), Instituto de Salud Carlos III, 28029 Madrid, Spain.
Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.

Classifications MeSH