Intravenous immunoglobulin treatment stabilizing a patient with Anti-PL7 antisynthetase syndrome with interstitial lung disease and eosinophilic inflammation.

Anti-PL7 Antisynthetase syndrome (AS) Eosinophilic inflammation Interstitial lung disease (ILD) Intravenous immunoglobulin (IVIG)

Journal

Respiratory medicine case reports
ISSN: 2213-0071
Titre abrégé: Respir Med Case Rep
Pays: England
ID NLM: 101604463

Informations de publication

Date de publication:
2022
Historique:
received: 07 02 2022
revised: 24 05 2022
accepted: 06 06 2022
entrez: 11 7 2022
pubmed: 12 7 2022
medline: 12 7 2022
Statut: epublish

Résumé

Antisynthetase syndrome (AS) is a rare autoimmune disease characterized by autoantibodies against aminoacyl-transfer RNA synthetase and clinical features which can include interstitial lung disease (ILD). Current available evidence of treatment is based on expert opinions and case reports. Here, we present a patient with an initial diagnosis of eosinophilic pneumonia, who was later diagnosed with anti-PL7 antisynthetase syndrome with ILD and eosinophilic inflammation. The patient was non-responsive to classic immunosuppressants but responded remarkably well to intravenous immunoglobulin.

Identifiants

pubmed: 35814032
doi: 10.1016/j.rmcr.2022.101686
pii: S2213-0071(22)00108-3
pmc: PMC9256658
doi:

Types de publication

Case Reports

Langues

eng

Pagination

101686

Informations de copyright

© 2022 The Authors.

Déclaration de conflit d'intérêts

None.

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Auteurs

Soran Peshbahar (S)

Diagnostic Centre, Silkeborg Regional Hospital, Falkevej 1-3, 8600, Silkeborg, Denmark.
Center for Rare Lung Diseases, Department of Respiratory Diseases and Allergy, Aarhus University Hospital, Palle Juul-Jensens Boulevard 99, 8200, Aarhus N, Denmark.

Charlotte Hyldgaard (C)

Diagnostic Centre, Silkeborg Regional Hospital, Falkevej 1-3, 8600, Silkeborg, Denmark.

Elisabeth Bendstrup (E)

Center for Rare Lung Diseases, Department of Respiratory Diseases and Allergy, Aarhus University Hospital, Palle Juul-Jensens Boulevard 99, 8200, Aarhus N, Denmark.

Classifications MeSH