Spontaneous NLRP3 inflammasome-driven IL-1-β secretion is induced in severe COVID-19 patients and responds to anakinra treatment.


Journal

The Journal of allergy and clinical immunology
ISSN: 1097-6825
Titre abrégé: J Allergy Clin Immunol
Pays: United States
ID NLM: 1275002

Informations de publication

Date de publication:
10 2022
Historique:
received: 18 08 2021
revised: 03 05 2022
accepted: 18 05 2022
pubmed: 15 7 2022
medline: 12 10 2022
entrez: 14 7 2022
Statut: ppublish

Résumé

Severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2) infection may result in a severe pneumonia associated with elevation of blood inflammatory parameters, reminiscent of cytokine storm syndrome. Steroidal anti-inflammatory therapies have shown efficacy in reducing mortality in critically ill patients; however, the mechanisms by which SARS-CoV-2 triggers such an extensive inflammation remain unexplained. To dissect the mechanisms underlying SARS-CoV-2-associated inflammation in patients with severe coronavirus disease 2019 (COVID-19), we studied the role of IL-1β, a pivotal cytokine driving inflammatory phenotypes, whose maturation and secretion are regulated by inflammasomes. We analyzed nod-like receptor protein 3 pathway activation by means of confocal microscopy, plasma cytokine measurement, cytokine secretion following in vitro stimulation of blood circulating monocytes, and whole-blood RNA sequencing. The role of open reading frame 3a SARS-CoV-2 protein was assessed by confocal microscopy analysis following nucleofection of a monocytic cell line. We found that circulating monocytes from patients with COVID-19 display ASC (adaptor molecule apoptotic speck like protein-containing a CARD) specks that colocalize with nod-like receptor protein 3 inflammasome and spontaneously secrete IL-1β in vitro. This spontaneous activation reverts following patient's treatment with the IL-1 receptor antagonist anakinra. Transfection of a monocytic cell line with cDNA coding for the ORF3a SARS-CoV-2 protein resulted in ASC speck formation. These results provide further evidence that IL-1β targeting could represent an effective strategy in this disease and suggest a mechanistic explanation for the strong inflammatory manifestations associated with COVID-19.

Sections du résumé

BACKGROUND
Severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2) infection may result in a severe pneumonia associated with elevation of blood inflammatory parameters, reminiscent of cytokine storm syndrome. Steroidal anti-inflammatory therapies have shown efficacy in reducing mortality in critically ill patients; however, the mechanisms by which SARS-CoV-2 triggers such an extensive inflammation remain unexplained.
OBJECTIVES
To dissect the mechanisms underlying SARS-CoV-2-associated inflammation in patients with severe coronavirus disease 2019 (COVID-19), we studied the role of IL-1β, a pivotal cytokine driving inflammatory phenotypes, whose maturation and secretion are regulated by inflammasomes.
METHODS
We analyzed nod-like receptor protein 3 pathway activation by means of confocal microscopy, plasma cytokine measurement, cytokine secretion following in vitro stimulation of blood circulating monocytes, and whole-blood RNA sequencing. The role of open reading frame 3a SARS-CoV-2 protein was assessed by confocal microscopy analysis following nucleofection of a monocytic cell line.
RESULTS
We found that circulating monocytes from patients with COVID-19 display ASC (adaptor molecule apoptotic speck like protein-containing a CARD) specks that colocalize with nod-like receptor protein 3 inflammasome and spontaneously secrete IL-1β in vitro. This spontaneous activation reverts following patient's treatment with the IL-1 receptor antagonist anakinra. Transfection of a monocytic cell line with cDNA coding for the ORF3a SARS-CoV-2 protein resulted in ASC speck formation.
CONCLUSIONS
These results provide further evidence that IL-1β targeting could represent an effective strategy in this disease and suggest a mechanistic explanation for the strong inflammatory manifestations associated with COVID-19.

Identifiants

pubmed: 35835255
pii: S0091-6749(22)00906-X
doi: 10.1016/j.jaci.2022.05.029
pmc: PMC9272569
pii:
doi:

Substances chimiques

Anti-Inflammatory Agents 0
Cytokines 0
DNA, Complementary 0
Inflammasomes 0
Interleukin 1 Receptor Antagonist Protein 0
Interleukin-1beta 0
NLR Family, Pyrin Domain-Containing 3 Protein 0
NLR Proteins 0
Receptors, Interleukin-1 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

796-805

Informations de copyright

Copyright © 2022 American Academy of Allergy, Asthma & Immunology. Published by Elsevier Inc. All rights reserved.

Références

Reproduction. 2005 Nov;130(5):721-9
pubmed: 16264101
Nature. 2022 Jun;606(7914):576-584
pubmed: 35385861
OMICS. 2012 May;16(5):284-7
pubmed: 22455463
Virology. 2022 Mar;568:13-22
pubmed: 35066302
J Immunol. 1987 Sep 15;139(6):1902-10
pubmed: 3497982
Cell Syst. 2015 Dec 23;1(6):417-425
pubmed: 26771021
Proc Natl Acad Sci U S A. 2005 Oct 25;102(43):15545-50
pubmed: 16199517
Lancet Rheumatol. 2020 Jun;2(6):e358-e367
pubmed: 32373790
Ann Rheum Dis. 2013 Jun;72(6):1064-70
pubmed: 23223423
Cell Host Microbe. 2020 Jun 10;27(6):992-1000.e3
pubmed: 32320677
Nat Genet. 2014 Oct;46(10):1140-6
pubmed: 25217959
Arthritis Rheumatol. 2020 Jul;72(7):1059-1063
pubmed: 32293098
J Immunol. 2015 Jan 1;194(1):455-62
pubmed: 25404358
Genome Biol. 2014;15(12):550
pubmed: 25516281
Nat Biotechnol. 2016 May;34(5):525-7
pubmed: 27043002
Sci Immunol. 2020 Sep 17;5(51):
pubmed: 32943497
Bioinformatics. 2011 Jun 15;27(12):1739-40
pubmed: 21546393
J Exp Med. 2021 Mar 1;218(3):
pubmed: 33231615
Nat Commun. 2021 Aug 2;12(1):4664
pubmed: 34341353
Proc Natl Acad Sci U S A. 2008 Jun 10;105(23):8067-72
pubmed: 18523012
J Clin Immunol. 2019 Jul;39(5):476-485
pubmed: 31144250
Pediatr Rheumatol Online J. 2017 Jan 17;15(1):5
pubmed: 28095869
Nat Med. 2021 Oct;27(10):1752-1760
pubmed: 34480127
Arthritis Rheum. 2007 Sep;56(9):3138-48
pubmed: 17763411
J Immunol. 1987 Sep 15;139(6):1911-7
pubmed: 3497983
Nat Rev Immunol. 2019 Aug;19(8):477-489
pubmed: 31036962
Cell Death Dis. 2018 Oct 23;9(11):1088
pubmed: 30352992
Nature. 2020 Aug;584(7821):463-469
pubmed: 32717743
Cell. 2020 Sep 17;182(6):1419-1440.e23
pubmed: 32810438
Cell. 2020 Sep 17;182(6):1401-1418.e18
pubmed: 32810439
FASEB J. 2019 Aug;33(8):8865-8877
pubmed: 31034780
J Allergy Clin Immunol. 2020 Jul;146(1):213-215
pubmed: 32437739
J Immunol. 2002 Feb 15;168(4):1984-91
pubmed: 11823535
Lancet Rheumatol. 2021 Oct;3(10):e690-e697
pubmed: 34396156
Cell Death Dis. 2016 Jul 21;7:e2304
pubmed: 27441656
Cell Host Microbe. 2020 Jun 10;27(6):879-882.e2
pubmed: 32359396
Clin Infect Dis. 2021 Aug 2;73(3):376-385
pubmed: 32463434
Blood. 2018 Mar 29;131(13):1442-1455
pubmed: 29326099
Lancet Rheumatol. 2020 Jun;2(6):e325-e331
pubmed: 32501454

Auteurs

Arinna Bertoni (A)

UOSD Centro per le Malattie Autoinfiammatorie e Immunodeficienze, IRCCS Istituto Giannina Gaslini, Genova, Italy; DINOGMI, Università degli Studi di Genova, Genova, Italy.

Federica Penco (F)

UOSD Centro per le Malattie Autoinfiammatorie e Immunodeficienze, IRCCS Istituto Giannina Gaslini, Genova, Italy.

Hilaria Mollica (H)

UOSD Centro per le Malattie Autoinfiammatorie e Immunodeficienze, IRCCS Istituto Giannina Gaslini, Genova, Italy; DINOGMI, Università degli Studi di Genova, Genova, Italy.

Paola Bocca (P)

UOSD Centro per le Malattie Autoinfiammatorie e Immunodeficienze, IRCCS Istituto Giannina Gaslini, Genova, Italy.

Ignazia Prigione (I)

UOSD Centro per le Malattie Autoinfiammatorie e Immunodeficienze, IRCCS Istituto Giannina Gaslini, Genova, Italy.

Anna Corcione (A)

UOSD Centro per le Malattie Autoinfiammatorie e Immunodeficienze, IRCCS Istituto Giannina Gaslini, Genova, Italy.

Davide Cangelosi (D)

Clinical Bioinformatics Unit and Diagnostics, IRCCS Istituto Giannina Gaslini, Genova, Italy.

Francesca Schena (F)

UOSD Centro per le Malattie Autoinfiammatorie e Immunodeficienze, IRCCS Istituto Giannina Gaslini, Genova, Italy.

Genny Del Zotto (G)

Department of Research and Diagnostics, IRCCS Istituto Giannina Gaslini, Genova, Italy.

Adriana Amaro (A)

IRCCS Ospedale Policlinico San Martino, Genova, Italy.

Noemi Paladino (N)

UOSD Centro per le Malattie Autoinfiammatorie e Immunodeficienze, IRCCS Istituto Giannina Gaslini, Genova, Italy.

Emanuele Pontali (E)

Ente Ospedaliero Ospedale Galliera, Genova, Italy.

Marcello Feasi (M)

Ente Ospedaliero Ospedale Galliera, Genova, Italy.

Sara Signa (S)

UOSD Centro per le Malattie Autoinfiammatorie e Immunodeficienze, IRCCS Istituto Giannina Gaslini, Genova, Italy; DINOGMI, Università degli Studi di Genova, Genova, Italy.

Marta Bustaffa (M)

UOSD Centro per le Malattie Autoinfiammatorie e Immunodeficienze, IRCCS Istituto Giannina Gaslini, Genova, Italy.

Roberta Caorsi (R)

UOSD Centro per le Malattie Autoinfiammatorie e Immunodeficienze, IRCCS Istituto Giannina Gaslini, Genova, Italy.

Serena Palmeri (S)

DINOGMI, Università degli Studi di Genova, Genova, Italy.

Paola Contini (P)

Department of Internal Medicine, University of Genoa and IRCCS IST-Ospedale San Martino, Genova, Italy.

Raffaele De Palma (R)

Department of Internal Medicine, University of Genoa and IRCCS IST-Ospedale San Martino, Genova, Italy.

Ulrich Pfeffer (U)

IRCCS Ospedale Policlinico San Martino, Genova, Italy.

Paolo Uva (P)

Clinical Bioinformatics Unit and Diagnostics, IRCCS Istituto Giannina Gaslini, Genova, Italy; Italian Institute of Technology, Genova, Italy.

Anna Rubartelli (A)

Istituto Giannina Gaslini, Genova, Italy.

Marco Gattorno (M)

UOSD Centro per le Malattie Autoinfiammatorie e Immunodeficienze, IRCCS Istituto Giannina Gaslini, Genova, Italy. Electronic address: marcogattorno@gaslini.org.

Stefano Volpi (S)

UOSD Centro per le Malattie Autoinfiammatorie e Immunodeficienze, IRCCS Istituto Giannina Gaslini, Genova, Italy; DINOGMI, Università degli Studi di Genova, Genova, Italy. Electronic address: stefanovolpi@gaslini.org.

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