[Recurrent epistaxis with coagulation disorders in a boy aged 2 years].
2岁男孩反复鼻衄伴凝血功能异常.
Child
Coagulation function
Epistaxis
Hypoprothrombinemia-lupus anticoagulant syndrome
Journal
Zhongguo dang dai er ke za zhi = Chinese journal of contemporary pediatrics
ISSN: 1008-8830
Titre abrégé: Zhongguo Dang Dai Er Ke Za Zhi
Pays: China
ID NLM: 100909956
Informations de publication
Date de publication:
15 Jul 2022
15 Jul 2022
Historique:
entrez:
27
7
2022
pubmed:
28
7
2022
medline:
29
7
2022
Statut:
ppublish
Résumé
A boy, aged 2 years and 5 months, had recurrent epistaxis, and the coagulation function examination showed that activated partial thromboplastin time (APTT) was significantly prolonged. Further laboratory examinations showed that the prolonged APTT was not immediately corrected in the APTT correction test, with positive lupus anticoagulant and low prothrombin activity. The boy was diagnosed with hypoprothrombinemia-lupus anticoagulant syndrome. The condition was improved after treatment with glucocorticoid, immunoglobulin, and vitamin K 2岁5个月男孩,反复鼻衄,凝血功能发现活化部分凝血活酶时间(activated partial thromboplastin time,APTT)明显延长,进一步实验室检查提示APTT纠正试验为即刻不能纠正,狼疮抗凝物检测阳性,凝血酶原活性低,诊断为低凝血酶原血症-狼疮抗凝物综合征。予激素、丙种球蛋白、维生素K
Autres résumés
Type: Publisher
(chi)
2岁5个月男孩,反复鼻衄,凝血功能发现活化部分凝血活酶时间(activated partial thromboplastin time,APTT)明显延长,进一步实验室检查提示APTT纠正试验为即刻不能纠正,狼疮抗凝物检测阳性,凝血酶原活性低,诊断为低凝血酶原血症-狼疮抗凝物综合征。予激素、丙种球蛋白、维生素K
Identifiants
pubmed: 35894199
pii: 1008-8830(2022)07-0817-04
doi: 10.7499/j.issn.1008-8830.2203060
pmc: PMC9336632
pii:
doi:
Substances chimiques
Lupus Coagulation Inhibitor
0
Prothrombin
9001-26-7
Types de publication
Case Reports
Journal Article
Langues
chi
Sous-ensembles de citation
IM
Pagination
817-820Références
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