In vitro modeling of amyotrophic lateral sclerosis with induced pluripotent stem cell technology-derived cell line ORIONi002-A.


Journal

Stem cell research
ISSN: 1876-7753
Titre abrégé: Stem Cell Res
Pays: England
ID NLM: 101316957

Informations de publication

Date de publication:
08 2022
Historique:
received: 09 03 2022
revised: 13 06 2022
accepted: 11 07 2022
pubmed: 31 7 2022
medline: 10 8 2022
entrez: 30 7 2022
Statut: ppublish

Résumé

We present here a new iPS cell line for modeling sporadic form of ALS. Cell line was generated by reprogramming skin fibroblasts isolated with explant culture technology from skin biopsy, donated by ALS patient. For reprogramming, polycistronic self-replicating RNA vector was used and derived iPS cells were characterized by immunocytochemistry and FACS (pluripotent factors expression), karyotyping, STR fingerprinting analysis and in vitro differentiation assay. New cell line showed normal (46, XY) karyotype and differentiated in vitro into cells from three germ layers. STR analysis proved the origin and originality of the cell line.

Identifiants

pubmed: 35907349
pii: S1873-5061(22)00219-7
doi: 10.1016/j.scr.2022.102870
pii:
doi:

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

102870

Informations de copyright

Copyright © 2022 The Author(s). Published by Elsevier B.V. All rights reserved.

Auteurs

Jan Strnadel (J)

Biomedical Centre Martin JFM CU, Jessenius Faculty of Medicine in Martin (JFM CU), Comenius University in Bratislava, Slovakia. Electronic address: jan.strnadel@uniba.sk.

Hugo M Dumortier (HM)

Biomedical Centre Martin JFM CU, Jessenius Faculty of Medicine in Martin (JFM CU), Comenius University in Bratislava, Slovakia.

Dominika Hajduchova (D)

Department of Pathological Physiology, Jessenius Faculty of Medicine in Martin (JFM CU), Comenius University in Bratislava, Slovakia.

Romana Zahumenska (R)

Biomedical Centre Martin JFM CU, Jessenius Faculty of Medicine in Martin (JFM CU), Comenius University in Bratislava, Slovakia.

Vladimir Nosal (V)

Clinic of Neurology, Comenius University in Bratislava, Jessenius Faculty of Medicine in Martin, University Hospital, Martin, Slovakia.

Marek Smolar (M)

Clinic of Surgery and Transplant Center, Comenius University in Bratislava, Jessenius Faculty of Medicine in Martin, University Hospital, Martin, Slovakia.

Juraj Marcinek (J)

Department of Pathological Anatomy, Comenius University in Bratislava, Jessenius Faculty of Medicine in Martin, University Hospital, Martin, Slovakia.

Michal Kalman (M)

Department of Pathological Anatomy, Comenius University in Bratislava, Jessenius Faculty of Medicine in Martin, University Hospital, Martin, Slovakia.

Sandra Mersakova (S)

Biomedical Centre Martin JFM CU, Jessenius Faculty of Medicine in Martin (JFM CU), Comenius University in Bratislava, Slovakia.

Dusan Brany (D)

Biomedical Centre Martin JFM CU, Jessenius Faculty of Medicine in Martin (JFM CU), Comenius University in Bratislava, Slovakia.

Stefan Juhas (S)

PIGMOD Centre, Institute of Animal Physiology and Genetics, Czech Academy of Sciences, v.v.i., Liběchov, Czech Republic.

Jana Juhasova (J)

PIGMOD Centre, Institute of Animal Physiology and Genetics, Czech Academy of Sciences, v.v.i., Liběchov, Czech Republic.

Hana Studenovska (H)

Department of Biomaterials and Bioanalogous Systems Institute of Macromolecular Chemistry, Czech Academy of Sciences, Prague, Czech Republic.

Barbora Mitruskova (B)

Department of Clinical Genetics, Comenius University in Bratislava, Jessenius Faculty of Medicine in Martin, University Hospital, Martin, Slovakia.

Stanislava Suroviakova (S)

Clinic of Children and Adolescents, Comenius University in Bratislava, Jessenius Faculty of Medicine in Martin, University Hospital, Martin, Slovakia.

Slavomira Novakova (S)

Biomedical Centre Martin JFM CU, Jessenius Faculty of Medicine in Martin (JFM CU), Comenius University in Bratislava, Slovakia.

Henrieta Skovierova (H)

Biomedical Centre Martin JFM CU, Jessenius Faculty of Medicine in Martin (JFM CU), Comenius University in Bratislava, Slovakia.

Egon Kurca (E)

Clinic of Neurology, Comenius University in Bratislava, Jessenius Faculty of Medicine in Martin, University Hospital, Martin, Slovakia.

Renata Pecova (R)

Department of Pathological Physiology, Jessenius Faculty of Medicine in Martin (JFM CU), Comenius University in Bratislava, Slovakia.

Lukas Plank (L)

Department of Pathological Anatomy, Comenius University in Bratislava, Jessenius Faculty of Medicine in Martin, University Hospital, Martin, Slovakia.

Erika Halasova (E)

Biomedical Centre Martin JFM CU, Jessenius Faculty of Medicine in Martin (JFM CU), Comenius University in Bratislava, Slovakia.

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Classifications MeSH