Diagnosing Joubert Syndrome in Two Adult Siblings: A Very Rare Case Report.

hypotonia joubert syndrome (js) joubert syndrome-related disorders (jsrds) molar tooth sign (mts) mri

Journal

Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737

Informations de publication

Date de publication:
Jul 2022
Historique:
accepted: 19 07 2022
entrez: 22 8 2022
pubmed: 23 8 2022
medline: 23 8 2022
Statut: epublish

Résumé

Joubert syndrome (JS) is a rare genetic disorder usually diagnosed during childhood. Adult Joubert syndrome is rare, and that too in siblings from a non-consanguineous marriage in their adulthood is extremely rare, with very few cases reported worldwide. The need for expensive imaging modality to aid diagnosis has also been cited as a drawback in diagnosing the condition in resource-poor areas. We describe the case of two adult siblings who came for other diseases and were diagnosed with Joubert syndrome.

Identifiants

pubmed: 35989767
doi: 10.7759/cureus.27042
pmc: PMC9388958
doi:

Types de publication

Case Reports

Langues

eng

Pagination

e27042

Informations de copyright

Copyright © 2022, Kannauje et al.

Déclaration de conflit d'intérêts

The authors have declared that no competing interests exist.

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Auteurs

Pankaj K Kannauje (PK)

General Medicine, All India Institute of Medical Sciences, Raipur, Raipur, IND.

Vinay Pandit (V)

General Medicine, All India Institute of Medical Sciences, Raipur, Raipur, IND.

Preetam Wasnik (P)

General Medicine, All India Institute of Medical Sciences, Raipur, Raipur, IND.

Saroj K Pati (SK)

Radiodiagnosis, All India Institute of Medical Sciences, Raipur, Raipur, IND.

Nanditha Venkatesan (N)

Internal Medicine, All India Institute of Medical Sciences, Raipur, Raipur, IND.

Classifications MeSH