Janus kinase 2 inhibition by pacritinib as potential therapeutic target for liver fibrosis.


Journal

Hepatology (Baltimore, Md.)
ISSN: 1527-3350
Titre abrégé: Hepatology
Pays: United States
ID NLM: 8302946

Informations de publication

Date de publication:
01 04 2023
Historique:
received: 02 02 2022
accepted: 03 08 2022
pubmed: 23 8 2022
medline: 22 3 2023
entrez: 22 8 2022
Statut: ppublish

Résumé

Janus kinase 2 (JAK2) signaling is increased in human and experimental liver fibrosis with portal hypertension. JAK2 inhibitors, such as pacritinib, are already in advanced clinical development for other indications and might also be effective in liver fibrosis. Here, we investigated the antifibrotic role of the JAK2 inhibitor pacritinib on activated hepatic stellate cells (HSCs) in vitro and in two animal models of liver fibrosis in vivo . Transcriptome analyses of JAK2 in human livers and other targets of pacritinib have been shown to correlate with profibrotic factors. Although transcription of JAK2 correlated significantly with type I collagen expression and other profibrotic genes, no correlation was observed for interleukin-1 receptor-associated kinase and colony-stimulating factor 1 receptor. Pacritinib decreased gene expression of fibrosis markers in mouse primary and human-derived HSCs in vitro . Moreover, pacritinib decreased the proliferation, contraction, and migration of HSCs. C 57 BL/6J mice received ethanol in drinking water (16%) or Western diet in combination with carbon tetrachloride intoxication for 7 weeks to induce alcoholic or nonalcoholic fatty liver disease. Pacritinib significantly reduced liver fibrosis assessed by gene expression and Sirius red staining, as well as HSC activation assessed by alpha-smooth muscle actin immunostaining in fibrotic mice. Furthermore, pacritinib decreased the gene expression of hepatic steatosis markers in experimental alcoholic liver disease. Additionally, pacritinib protected against liver injury as assessed by aminotransferase levels. This study demonstrates that the JAK2 inhibitor pacritinib may be promising for the treatment of alcoholic and nonalcoholic liver fibrosis and may be therefore relevant for human pathology.

Sections du résumé

BACKGROUND AND AIMS
Janus kinase 2 (JAK2) signaling is increased in human and experimental liver fibrosis with portal hypertension. JAK2 inhibitors, such as pacritinib, are already in advanced clinical development for other indications and might also be effective in liver fibrosis. Here, we investigated the antifibrotic role of the JAK2 inhibitor pacritinib on activated hepatic stellate cells (HSCs) in vitro and in two animal models of liver fibrosis in vivo .
APPROACH AND RESULTS
Transcriptome analyses of JAK2 in human livers and other targets of pacritinib have been shown to correlate with profibrotic factors. Although transcription of JAK2 correlated significantly with type I collagen expression and other profibrotic genes, no correlation was observed for interleukin-1 receptor-associated kinase and colony-stimulating factor 1 receptor. Pacritinib decreased gene expression of fibrosis markers in mouse primary and human-derived HSCs in vitro . Moreover, pacritinib decreased the proliferation, contraction, and migration of HSCs. C 57 BL/6J mice received ethanol in drinking water (16%) or Western diet in combination with carbon tetrachloride intoxication for 7 weeks to induce alcoholic or nonalcoholic fatty liver disease. Pacritinib significantly reduced liver fibrosis assessed by gene expression and Sirius red staining, as well as HSC activation assessed by alpha-smooth muscle actin immunostaining in fibrotic mice. Furthermore, pacritinib decreased the gene expression of hepatic steatosis markers in experimental alcoholic liver disease. Additionally, pacritinib protected against liver injury as assessed by aminotransferase levels.
CONCLUSIONS
This study demonstrates that the JAK2 inhibitor pacritinib may be promising for the treatment of alcoholic and nonalcoholic liver fibrosis and may be therefore relevant for human pathology.

Identifiants

pubmed: 35993369
pii: 01515467-202304000-00019
doi: 10.1002/hep.32746
pmc: PMC10026969
doi:

Substances chimiques

11-(2-pyrrolidin-1-ylethoxy)-14,19-dioxa-5,7,26-triazatetracyclo(19.3.1.1(2,6).1(8,12))heptacosa-1(25),2(26),3,5,8,10,12(27),16,21,23-decaene 0
Janus Kinase 2 EC 2.7.10.2
Bridged-Ring Compounds 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

1228-1240

Informations de copyright

Copyright © 2023 The Author(s). Published by Wolters Kluwer Health, Inc.

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Auteurs

Sandra Torres (S)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.
Department of Cell Death and Proliferation , Instituto Investigaciones Biomédicas de Barcelona (IIBB), Spanish National Research Council (CSIC) , Barcelona , Spain.
Liver Unit-IDIBAPS and Centro de Investigación Biomédica en Red (CIBERehd) , Barcelona , Spain.

Cristina Ortiz (C)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.

Nadine Bachtler (N)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.

Wenyi Gu (W)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.
Department of Internal Medicine B , University of Münster , Münster , Germany.

Leon D Grünewald (LD)

Department of Diagnostic and Interventional Radiology , Universit+y Hospital Frankfurt , Frankfurt am Main , Germany.

Nico Kraus (N)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.

Robert Schierwagen (R)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.
Department of Internal Medicine B , University of Münster , Münster , Germany.

Christoph Hieber (C)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.

Caroline Meier (C)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.

Olaf Tyc (O)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.

Maximilian Joseph Brol (M)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.
Department of Internal Medicine B , University of Münster , Münster , Germany.

Frank Erhard Uschner (FE)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.
Department of Internal Medicine B , University of Münster , Münster , Germany.

Bart Nijmeijer (B)

Research and Development Department , Linxis BV , Amsterdam , The Netherlands.

Christoph Welsch (C)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.

Marie-Luise Berres (ML)

Department of Internal Medicine III , Aachen University Hospital , Aachen , Germany.

Carmen Garcia-Ruiz (C)

Department of Cell Death and Proliferation , Instituto Investigaciones Biomédicas de Barcelona (IIBB), Spanish National Research Council (CSIC) , Barcelona , Spain.
Liver Unit-IDIBAPS and Centro de Investigación Biomédica en Red (CIBERehd) , Barcelona , Spain.
Department of Medicine , University of Southern California, Research Center for Alcoholic Liver and Pancreatic Diseases and Cirrhosis, Keck School of Medicine, University of Southern California , Los Angeles , California , USA.

Jose Carlos Fernandez-Checa (JC)

Department of Cell Death and Proliferation , Instituto Investigaciones Biomédicas de Barcelona (IIBB), Spanish National Research Council (CSIC) , Barcelona , Spain.
Liver Unit-IDIBAPS and Centro de Investigación Biomédica en Red (CIBERehd) , Barcelona , Spain.
Department of Medicine , University of Southern California, Research Center for Alcoholic Liver and Pancreatic Diseases and Cirrhosis, Keck School of Medicine, University of Southern California , Los Angeles , California , USA.

Christian Trautwein (C)

Department of Internal Medicine III , Aachen University Hospital , Aachen , Germany.

Thomas J Vogl (TJ)

Department of Diagnostic and Interventional Radiology , Universit+y Hospital Frankfurt , Frankfurt am Main , Germany.

Stefan Zeuzem (S)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.

Jonel Trebicka (J)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.
Department of Internal Medicine B , University of Münster , Münster , Germany.
European Foundation for the Study of Chronic Liver Failure - EF Clif , Barcelona , Spain.

Sabine Klein (S)

Department of Internal Medicine I , Goethe University Clinic Frankfurt , Frankfurt , Germany.
Department of Internal Medicine B , University of Münster , Münster , Germany.

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