Leber Hereditary Optic Neuropathy: Molecular Pathophysiology and Updates on Gene Therapy.

gene therapy leber hereditary optic neuropathy molecular pathophysiology

Journal

Biomedicines
ISSN: 2227-9059
Titre abrégé: Biomedicines
Pays: Switzerland
ID NLM: 101691304

Informations de publication

Date de publication:
09 Aug 2022
Historique:
received: 24 06 2022
revised: 29 07 2022
accepted: 04 08 2022
entrez: 26 8 2022
pubmed: 27 8 2022
medline: 27 8 2022
Statut: epublish

Résumé

Molecular pathophysiology of LHON was reviewed and the current status of gene therapy for LHON is updated.

Identifiants

pubmed: 36009477
pii: biomedicines10081930
doi: 10.3390/biomedicines10081930
pmc: PMC9405679
pii:
doi:

Types de publication

Journal Article Review

Langues

eng

Déclaration de conflit d'intérêts

A.G.W was the PI of the REFLECT trial. H.C.C was the co-PI of the REFLECT trial.

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Auteurs

Sheng-Chu Chi (SC)

Department of Ophthalmology, Taipei Veterans General Hospital, Taipei 112, Taiwan.

Hui-Chen Cheng (HC)

Department of Ophthalmology, Taipei Veterans General Hospital, Taipei 112, Taiwan.
Department of Ophthalmology, School of Medicine, National Yang Ming Chiao Tung University, Taipei 112, Taiwan.
Program in Molecular Medicine, College of Life Sciences, National Yang Ming Chiao Tung University, Taipei 112, Taiwan.
Department of Life Sciences and Institute of Genome Sciences, College of Life Sciences, National Yang Ming Chiao Tung University, Taipei 112, Taiwan.
Brain Research Center, National Yang Ming Chiao Tung University, Taipei 112, Taiwan.

An-Guor Wang (AG)

Department of Ophthalmology, Taipei Veterans General Hospital, Taipei 112, Taiwan.
Department of Ophthalmology, School of Medicine, National Yang Ming Chiao Tung University, Taipei 112, Taiwan.

Classifications MeSH