When Autoimmunity 'DRESSes up': A Case after Certolizumab Therapy.

Drug Reaction with Eosinophilia and Systemic Symptoms (DRESS) certolizumab eosinophilia lymphadenopathy rheumatoid arthritis

Journal

European journal of case reports in internal medicine
ISSN: 2284-2594
Titre abrégé: Eur J Case Rep Intern Med
Pays: Italy
ID NLM: 101648453

Informations de publication

Date de publication:
2022
Historique:
received: 15 06 2022
accepted: 27 06 2022
entrez: 2 9 2022
pubmed: 3 9 2022
medline: 3 9 2022
Statut: epublish

Résumé

Drug Reaction with Eosinophilia and Systemic Symptoms (DRESS) is characterised by skin rash together with visceral organ involvement, lymphadenopathy, eosinophilia and atypical lymphocytosis. The syndrome is clinically heterogeneous, making diagnosis challenging. It has an annual incidence of 2 per 100,000 population and a mortality rate of 2-10%. We describe the first case of DRESS induced by certolizumab, a biologic disease-modifying antirheumatic drug (bioDMARD). Drug Reaction with Eosinophilia and Systemic Symptoms (DRESS) is an uncommon and under-reported syndrome.Its recognition is critical for treatment, especially in the emergency setting where most patients first present.In the case of unexplained fever, lymphadenopathy, cutaneous rash and characteristic laboratory findings (e.g., eosinophilia), after infectious causes have been ruled out, clinicians should always keep DRESS in mind and consider possible recent intake of a triggering drug.

Identifiants

pubmed: 36051169
doi: 10.12890/2022_003451
pii: 3451-1-29566-1-10-20220713
pmc: PMC9426962
doi:

Types de publication

Journal Article

Langues

eng

Pagination

003451

Informations de copyright

© EFIM 2022.

Déclaration de conflit d'intérêts

Conflicts of Interests: The Authors declare that there are no competing interest

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Auteurs

Benedetta Marigliano (B)

UOC Pronto Soccorso e Medicina d'Urgenza, Azienda Ospedaliera San Camillo - Forlanini, Rome, Italy.

Federico Rosa (F)

UOC Pronto Soccorso e Medicina d'Urgenza, Fondazione Policlinico Universitario Agostino Gemelli IRCCS, Rome, Italy.

Mattia Internullo (M)

UOC Pronto Soccorso e Medicina d'Urgenza, Azienda Ospedaliera San Camillo - Forlanini, Rome, Italy.

Luigi Scuro (L)

UOC Pronto Soccorso e Medicina d'Urgenza, Azienda Ospedaliera San Camillo - Forlanini, Rome, Italy.

Andrea Tavanti (A)

UOC Pronto Soccorso e Medicina d'Urgenza, Azienda Ospedaliera San Camillo - Forlanini, Rome, Italy.

Lucia Rita Del Vecchio (LR)

UOC Pronto Soccorso e Medicina d'Urgenza, Azienda Ospedaliera San Camillo - Forlanini, Rome, Italy.

Francesco Paolo Romagno (FP)

UOC Pronto Soccorso e Medicina d'Urgenza, Azienda Ospedaliera San Camillo - Forlanini, Rome, Italy.

Maria Barbara Schito (MB)

UOC Pronto Soccorso e Medicina d'Urgenza, Azienda Ospedaliera San Camillo - Forlanini, Rome, Italy.

Federica Pace (F)

UOC Pronto Soccorso e Medicina d'Urgenza, Azienda Ospedaliera San Camillo - Forlanini, Rome, Italy.

Giovanni Maria Colombo (GM)

UOC Pronto Soccorso e Medicina d'Urgenza, Azienda Ospedaliera San Camillo - Forlanini, Rome, Italy.

Emanuele Guglielmelli (E)

UOC Pronto Soccorso e Medicina d'Urgenza, Azienda Ospedaliera San Camillo - Forlanini, Rome, Italy.

Classifications MeSH