Development of versatile allele-specific siRNAs able to silence all the dominant dynamin 2 mutations.

MT: RNA/DNA Editing RNA interference adhesion allele-specific silencing dominant centronuclear myopathy dynamin 2 endocytosis gene therapy migration

Journal

Molecular therapy. Nucleic acids
ISSN: 2162-2531
Titre abrégé: Mol Ther Nucleic Acids
Pays: United States
ID NLM: 101581621

Informations de publication

Date de publication:
13 Sep 2022
Historique:
received: 28 03 2022
accepted: 10 08 2022
entrez: 12 9 2022
pubmed: 13 9 2022
medline: 13 9 2022
Statut: epublish

Résumé

Dominant centronuclear myopathy (CNM) is a rare form of congenital myopathy associated with a wide clinical spectrum, from severe neonatal to milder adult forms. There is no available treatment for this disease due to heterozygous mutations in the

Identifiants

pubmed: 36090755
doi: 10.1016/j.omtn.2022.08.016
pii: S2162-2531(22)00215-3
pmc: PMC9439966
doi:

Types de publication

Journal Article

Langues

eng

Pagination

733-748

Informations de copyright

© 2022 The Authors.

Déclaration de conflit d'intérêts

The authors declare no competing interests.

Références

FASEB J. 2021 Apr;35(4):e21346
pubmed: 33715228
Traffic. 2011 Nov;12(11):1620-33
pubmed: 21762456
Biochem Biophys Res Commun. 2014 Jan 10;443(2):511-7
pubmed: 24316215
Med Sci Monit. 2020 Aug 22;26:e924590
pubmed: 32827429
EMBO Mol Med. 2018 Feb;10(2):239-253
pubmed: 29246969
Proc Natl Acad Sci U S A. 2014 May 6;111(18):E1872-9
pubmed: 24753582
EMBO J. 2010 Sep 15;29(18):3054-67
pubmed: 20700106
Hum Gene Ther. 2008 Jul;19(7):710-9
pubmed: 18549309
J Cell Sci. 2009 Oct 1;122(Pt 19):3427-31
pubmed: 19759282
J Biol Chem. 2010 Jul 23;285(30):22753-7
pubmed: 20529869
Hum Mutat. 2009 Oct;30(10):1419-27
pubmed: 19623537
Mol Ther Nucleic Acids. 2019 Jun 7;16:246-256
pubmed: 30925452
PLoS One. 2014 Feb 19;9(2):e89073
pubmed: 24586511
Oncogene. 2012 Mar 8;31(10):1228-41
pubmed: 21841817
Cancer Med. 2014 Feb;3(1):14-24
pubmed: 24402972
FASEB J. 2019 Jul;33(7):8504-8518
pubmed: 31017801
PLoS One. 2014 Jun 13;9(6):e99341
pubmed: 24926995
J Exp Clin Cancer Res. 2021 Jul 22;40(1):238
pubmed: 34294140
Semin Pediatr Neurol. 2011 Dec;18(4):250-6
pubmed: 22172420
BMC Neurol. 2015 Oct 30;15:223
pubmed: 26517984
Dev Cell. 2009 Dec;17(6):811-22
pubmed: 20059951
Methods Enzymol. 2012;504:183-200
pubmed: 22264535
J Clin Invest. 2018 Dec 3;128(12):5307-5321
pubmed: 30371505
Nat Genet. 2005 Nov;37(11):1207-9
pubmed: 16227997
Nat Rev Mol Cell Biol. 2012 Jan 11;13(2):75-88
pubmed: 22233676
Curr Gene Ther. 2015;15(5):503-10
pubmed: 26264709
Proc Natl Acad Sci U S A. 2010 Dec 14;107(50):21731-6
pubmed: 21098280
Oncol Lett. 2019 Jul;18(1):219-226
pubmed: 31289491
Biochem Biophys Res Commun. 2016 Nov 18;480(3):409-414
pubmed: 27771248
Neuromuscul Disord. 2007 May;17(5):368-75
pubmed: 17383182
Brain. 2012 May;135(Pt 5):1395-411
pubmed: 22451505
J Neurol. 2011 Jun;258(6):1085-90
pubmed: 21221624
Cancer Res. 2019 Jun 1;79(11):2878-2891
pubmed: 30975647
Oncotarget. 2015 Sep 15;6(27):24560-70
pubmed: 26009994
BMC Mol Biol. 2012 Mar 07;13:6
pubmed: 22397573
Mol Biol Cell. 2020 Mar 15;31(6):439-451
pubmed: 31967944
J Mol Med (Berl). 2010 Apr;88(4):339-50
pubmed: 20127478
J Clin Invest. 2014 Mar;124(3):1350-63
pubmed: 24569376
Hum Mutat. 2012 Jun;33(6):949-59
pubmed: 22396310
Mol Biol Cell. 2003 Mar;14(3):1074-84
pubmed: 12631724
Eur J Hum Genet. 2014 Dec;22(12):1369-75
pubmed: 24667781
Mol Ther. 2010 Feb;18(2):442-6
pubmed: 19935778
Exp Neurol. 2009 Jun;217(2):312-9
pubmed: 19289118
Nat Genet. 2005 Mar;37(3):289-94
pubmed: 15731758
Int J Oncol. 2016 Sep;49(3):877-86
pubmed: 27572123
Dev Cell. 2013 Mar 25;24(6):573-85
pubmed: 23537630
Ann Neurol. 2007 Dec;62(6):666-70
pubmed: 17932957

Auteurs

Swati Dudhal (S)

Sorbonne Université, Inserm, Institut de Myologie, Centre de Recherche en Myologie, 75013 Paris, France.

Lylia Mekzine (L)

Sorbonne Université, Inserm, Institut de Myologie, Centre de Recherche en Myologie, 75013 Paris, France.

Bernard Prudhon (B)

Sorbonne Université, Inserm, Institut de Myologie, Centre de Recherche en Myologie, 75013 Paris, France.

Karishma Soocheta (K)

Sorbonne Université, Inserm, Institut de Myologie, Centre de Recherche en Myologie, 75013 Paris, France.

Bruno Cadot (B)

Sorbonne Université, Inserm, Institut de Myologie, Centre de Recherche en Myologie, 75013 Paris, France.

Kamel Mamchaoui (K)

Sorbonne Université, Inserm, Institut de Myologie, Centre de Recherche en Myologie, 75013 Paris, France.

Delphine Trochet (D)

Sorbonne Université, Inserm, Institut de Myologie, Centre de Recherche en Myologie, 75013 Paris, France.

Marc Bitoun (M)

Sorbonne Université, Inserm, Institut de Myologie, Centre de Recherche en Myologie, 75013 Paris, France.

Classifications MeSH